Definition (CHV)
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a condition that produces excessive red blood cells
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Definition (CHV)
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a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (CHV)
|
a condition that produces excessive red blood cells
|
Definition (MSHCZE)
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Krevní onemocnění charakterizované zvýšenou tvorbou červených krvinek, ale též některých bílých krvinek, granulocytů a krevních destiček v kostní dřeni a jejich zmnožením v krvi. Druh myeloproliferativního onemocnění, hladina erytropoetinu je na rozdíl od sekundární polycytemie nízká. Probíhá chronicky, kromě celkových příznaků bývají zejm. oběhové poruchy způsobené zvýšenou viskozitou krve a jejím větším množstvím a krvácivé či trombotické komplikace; může být hyperurikemie. Nápadný je vzhled nemocných s výraznou pletorou. Po řadě let někdy vyústí v jiné, závažnější krevní onemocnění charakteru leukemie nebo do fibrózy kostní dřeně. Léčí se opakovanými krevními odběry, erytrocytaferézou, některými cytostatiky či podáním radioaktivního fosforu. (cit. Velký lékařský slovník online, 2012 http://lekarske.slovniky.cz/ )
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Definition (NCI_NCI-GLOSS)
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A disease in which there are too many red blood cells in the bone marrow and blood, causing the blood to thicken. The number of white blood cells and platelets may also increase. The extra blood cells may collect in the spleen and cause it to become enlarged. They may also cause bleeding problems and make clots form in blood vessels.
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Definition (NCI)
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A chronic myeloproliferative neoplasm characterized by an increased red blood cell production. Excessive proliferation of the myeloid lineage is observed as well. The major symptoms are related to hypertension or to vascular abnormalities caused by the increased red cell mass. The cause is unknown. With currently available treatment, the median survival exceeds 10 years. (WHO, 2001)
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Definition (MSH)
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A myeloproliferative disorder of unknown etiology, characterized by abnormal proliferation of all hematopoietic bone marrow elements and an absolute increase in red cell mass and total blood volume, associated frequently with splenomegaly, leukocytosis, and thrombocythemia. Hematopoiesis is also reactive in extramedullary sites (liver and spleen). In time myelofibrosis occurs.
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Definition (CSP)
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myeloproliferative disorder characterized by abnormal proliferation of all hematopoietic bone marrow elements and an absolute increase in red cell mass and total blood volume; associated frequently with splenomegaly, leukocytosis, and thrombocythemia.
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Concepts |
Neoplastic Process
(T191)
|
MSH |
D011087
|
ICD9 |
238.4 |
ICD10 |
D45
, M9950/1 |
SnomedCT |
31569001, 278190000, 134182002, 269652000, 154644004, 109992005, 128841001 |
English |
Osler Vaquez Disease, Osler-Vaquez Disease, Disease, Osler-Vaquez, Erythremia, Erythremias, PPP-Primary prolif polycythaem, Prim proliferat polycythaemia, Prim proliferat polycythemia, Erythraemia, POLYCYTHEMIA RUBRA VERA, POLYCYTHEMIA VERA, PRV, OSLER VAQUEZ DIS, [M]Polycythaemia rubra vera, [M]Polycythaemia vera, [M]Polycythemia rubra vera, [M]Polycythemia vera, polycythemia vera, polycythemia vera (diagnosis), Polycythaemia vera -RETIRED-, Primary polycythemia, Polycythemia Vera [Disease/Finding], Vera, Polycythemia Rubra, Polycythemia Rubra Veras, Polycythemia Rubra Vera, Veras, Polycythemia Rubra, erythraemia, polycythaemia vera, proliferative polycythemia, vaquez's disease, p vera, primary polycythemia, splenomegalic polycythemia, erythrocythemia, osler's disease, Polycythemia Ruba Vera, Primary Polycythemia, Erythremia (morphologic abnormality), [M]Polycythemia vera (morphologic abnormality), PV, Polycythemia rubra vera, Polycythemia vera, Osler's disease, Vaquez's disease, PPP - Primary proliferative polycythaemia, PPP - Primary proliferative polycythemia, PRV - Polycythaemia rubra vera, PRV - Polycythemia rubra vera, Polycythaemia rubra vera, Polycythaemia vera, Primary proliferative polycythaemia, Primary proliferative polycythemia, Chronic erythraemia [obs], Chronic erythremia [obs], Osler-Vaquez syndrome, Polycythaemia vera (clinical), Polycythemia vera (clinical), Polycythemia vera (disorder), Polycythemia vera (morphologic abnormality), Proliferative polycythaemia, Proliferative polycythemia, p.vera, polycythemia ruba vera, Osler-Vaquez, Vaquez-Osler, erythremia, polycythemia; rubra vera, polycythemia; vera, rubra; polycythemia rubra vera, vera; polycythemia, Polycythemia vera -RETIRED-, Polycythemia Vera, Primary polycythaemia, polycythaemia rubra vera, polycythemia rubra vera |
Dutch |
primaire polycytemie, polycythaemia rubra vera, polycytemie vera, polycytemie rubra vera, ziekte van Vaquez, polycytemie; rubra vera, polycytemie; vera, rubra; polycythaemia rubra vera, vera; polycythaemia vera, polycythaemia vera, Erythremie, Polycythaemia vera, Vasquez-Osler-ziekte, Ziekte van Vasquez-Osler |
French |
Polyglobulie essentielle, Maladie de Vasquez, Polyglobulie primaire, Polyglobulie primitive, Polycythémie vraie, Polyglobulie primitive essentielle, Maladie de Vaquez, Polyglobulie vraie |
German |
Polycythaemia rubra vera, primaere Polyzythaemie, Vaquez Syndrom, Polycathaemia vera, Polycythaemia vera, Vasquez-Osler-Syndrom, Erythrämie |
Italian |
Policitemia primitiva, Malattia di Vasquez, Malattia di Osler-Vaquez, Eritremia, Policitemia vera |
Portuguese |
Policitemia rubra vera, Policitemia primária, Doença de Vaquez, Policitemia Rubra Vera, Policitemia vera, Doença de Osler-Vasquez, Eritremia, Policitemia Vera |
Spanish |
Policitemia rubra vera, Policitemia primaria, Enfermedad de Vázquez, Policitemia rubra verdadera, Policitemia verdadera, Policitemia Rubra Vera, [M] policitemia vera, policitemia vera (concepto no activo), eritremia, policitemia rubra vera (anomalía morfológica), eritremia (anomalía morfológica), policitemia rubra vera, eritremia crónica, eritrocitemia, policitemia proliferativa, policitemia vera (clínica), policitemia vera (trastorno), policitemia vera, policitemia verdadera (anomalía morfológica), policitemia verdadera (clínica), policitemia verdadera (trastorno), policitemia verdadera, síndrome de Osler - Vasquez, Policitemia vera, Enfermedad de Osler-Vaquez, Eritremia, Policitemia Vera |
Japanese |
原発性多血症, 原発性赤血球増加症, ゲンパツセイタケツショウ, ゲンパツセイセッケッキュウゾウカショウ, バケービョウ, シンセイタケツショウ, シンセイセッケッキュウゾウカショウ, オスラー・ワーケ病, オスラー・バケー病, Osler-Vaquez病, 多血症-真性, 真性多血症, 真性赤血球増加症, 真正多血症, 真正赤血球増加症, 赤血球増加症-真性, 赤血病-慢性, 赤血病, オスラー-ワーケ病, バケー-オスラー病, バケー病, 多血症-真正 |
Swedish |
Polycytemia vera
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Czech |
polycythemia vera, Vasquezova choroba, Polycytemia vera, Primární polycytemie, Polycytemia rubra vera, polycythaemia vera, Oslerova-Vaquezova nemoc, polycythaemia rubra vera, pravá polycytemie |
Finnish |
Itsenäinen polysytemia
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Russian |
ERITREMIIA, OSLERA-VAKEZA BOLEZN', POLITSITEMIIA ISTINNAIA, ОСЛЕРА-ВАКЕЗА БОЛЕЗНЬ, ПОЛИЦИТЕМИЯ ИСТИННАЯ, ЭРИТРЕМИЯ |
Korean |
진성 적혈구 증가증
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Croatian |
POLICITEMIJA RUBRA VERA
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Polish |
Choroba Oslera-Vaqueza, Czerwienica prawdziwa |
Hungarian |
Polycythaemia rubra vera, Primaer polycythaemia, Vaquez-betegség, Polycytemia rubra vera, Elsődleges polycythaemia, Polycythaemia vera |
Norwegian |
Polycythaemia rubra vera, Polycythaemia vera |