Definition (NCI)
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A partial or complete replacement of the bone marrow stroma by fibrous tissue. It can be a primary bone marrow lesion as part of the chronic myeloproliferative disorders (chronic idiopathic myelofibrosis), a manifestation of acute myeloid leukemia (acute panmyelosis with myelofibrosis), or a secondary phenomenon due to bone marrow involvement by a metastatic tumor (e.g., metastatic breast carcinoma). --2003
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Definition (NCI_NCI-GLOSS)
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A disorder in which the bone marrow is replaced by fibrous tissue.
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Definition (CSP)
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replacement of the bone marrow by fibrous tissue, occurring in association with a myeloproliferative disorder or secondary to another unrelated condition.
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Concepts |
Neoplastic Process
(T191)
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MSH |
D009191
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ICD9 |
289.83, 238.76 |
ICD10 |
D75.81
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SnomedCT |
267572005, 78956007, 154841009, 52967002 |
English |
Myelofibrosis, Agnogenic myeloid metaplasia, Myelofibrosis with myeloid metaplasia, Myelosis-non-leukemic, myelofibrosis, myelofibrosis (diagnosis), Myelosis non-leukaemic, Myelosis-non-leukaemic, Myelosis non-leukemic, Myelosis nonleukemic, MMM, MYELOFIBROSIS, MYELOFIBROSIS WITH MYELOID METAPLASIA, Myelofibrosis NOS, chronic idiopathic myelofibrosis, fibrosis bone marrow, bone fibrosis marrow, bone marrow fibrosis, mos, Myelosclerosis (disorder), Myelosclerosis, MF - Myelofibrosis, Myelofibrosis (disorder), myelosclerosis, Myelofibrosis, NOS, Myelosclerosis, NOS |
French |
MYELOFIBROSE, Myélose non leucémique, Myélofibrose |
Portuguese |
MIELOFIBROSE, Mielose não leucémica, Mielofibrose |
Spanish |
MIELOFIBROSIS, Mielosis no leucémica, mielosclerosis (concepto no activo), mielosclerosis, esclerosis de la médula ósea, fibrosis de la médula ósea, mielofibrosis (trastorno), mielofibrosis, Mielofibrosis |
German |
MYELOFIBROSE, Myelose nicht-leukaemisch, Myelofibrose |
Italian |
Mielofibrosi, Mielosi non leucemica |
Dutch |
myelosis niet-leukemisch, myelosis-niet-leukaemisch, myelosis niet-leukaemisch, myelofibrose |
Japanese |
骨髄線維症, コツズイセンイショウ, 非白血病性骨髄症, ヒハッケツビョウセイコツズイショウ |
Finnish |
Myelofibroosi
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Czech |
Neleukemická myelóza, Myelofibróza |
Hungarian |
Nem leukaemiás myelosis, Nem-leukaemiás myelosis, Myelofibrosis, Nem leukemiás myelosis, Nem-leukemiás myelosis |