II. Pathophysiology

  1. Deoxygenated, stagnating blood in dermal, dilated capillary blood vessels

III. Signs

  1. Characteristics
    1. Recurrent purple, red or blue discoloration of the skin in a reticular, lacy, fishnet pattern
    2. Skin Ulceration may occur
  2. Distribution
    1. Lower extremities most commonly involved
    2. May also affect upper extremities and trunk
  3. Provocative
    1. Cold exposure
      1. Cutis Marmorata refers to idiopathic onset with cold
  4. Palliative
    1. Idiopathic types improve more with rewarming than secondary types

IV. Causes

  1. Idiopathic (Cutis Marmorata)
    1. Cold exposure onset and resolves with warming
    2. Benign, without underlying Vasculitis
  2. Secondary Livedo Reticularis
    1. Lupus erythematosus
    2. Rheumatoid Arthritis
    3. Cryoglobulinemia
    4. Lymphoma
    5. Polycythemia Vera
    6. Polyarteritis Nodosa

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Ontology: Livedo Reticularis (C0085642)

Definition (NCI) A recurrent purple discoloration of the skin that does not blanche and is found in a lacy, network pattern, most often in the lower extremities. It may be aggravated by exposure to cold and is classified as idiopathic or secondary. Secondary livedo reticularis may be a cutaneous manifestation of immune system disorders (e.g., lupus erythematosus, rheumatoid arthritis, cryoglobulinemia, lymphoma, etc), and hematologic disorders (polycythemia vera).
Definition (MSH) A condition characterized by a reticular or fishnet pattern on the skin of lower extremities and other parts of the body. This red and blue pattern is due to deoxygenated blood in unstable dermal blood vessels. The condition is intensified by cold exposure and relieved by rewarming.
Concepts Disease or Syndrome (T047)
MSH D054068 , D017445
SnomedCT 279990005, 201303000, 238772004, 78820005
English LIVEDO RETICULARIS, livedo reticularis (physical finding), livedo reticularis, livedo reticularis (diagnosis), Livedo Reticularis [Disease/Finding], livedo racemosa, Livedo reticularis, Livedo racemosa, Livedo reticularis (disorder), asphyxia; reticularis, reticularis; asphyxia, Livedo reticularis, NOS, Livedo Reticularis
Spanish LIVEDO RETICULARIS, Livedo Reticularis, livedo racemosa, livedo reticularis (trastorno), livedo reticularis, Livedo reticularis
Italian Livedo reticularis, Livedo Reticularis
Japanese 網状皮斑, モウジョウヒハン
Portuguese Livedo Reticular, LIVEDO RETICULARIS, Livedo reticular
Finnish Verkkomainen lyijynsinisyys
French Livedo réticulaire, Livedo reticularis, LIVEDO, Livedo
German Livedo reticularis, LIVEDO RETICULARIS, Livedo retikularis
Russian KOZHA MRAMORNAIA SETCHATAIA, КОЖА МРАМОРНАЯ СЕТЧАТАЯ
Czech Livedo retikularis, livedo reticularis
Swedish Livedo reticularis
Polish Sinica siateczkowata, Sinica marmurkowata
Hungarian Livedo reticularis
Norwegian Livedo reticularis
Dutch asfyxie; reticularis, reticularis; asfyxie, livedo reticularis, Livedo reticularis