II. Definitions

  1. Cutis Marmorata
    1. Normal cold response in newborns that resolves with rewarming (may also be seen in adults)
    2. Symmetric skin mottling involving an infant's trunk and extremities

III. Epidemiology

  1. Occurs in the first few weeks of life when exposed to cold

IV. Physiology

  1. Normal newborn physiologic response to cold
  2. Capillaries and venules dilate in response to cold skin

V. Symptoms

  1. Episodic mottling with cold exposure for the first few months of life

VI. Signs

  1. Skin mottling symmetrically involving the trunk and extremities on cold exposure
  2. Resolves in warm Temperatures

VII. Differential Diagnosis

  1. Telangiectatica Congenita
    1. Rare, serious vascular anomaly with similar mottling as with Cutis Marmorata
    2. In contrast, Telangiectatica Congenita is associated with skin atrophy, Skin Ulceration or unilateral involvement
    3. Refer suspected cases

VIII. Management

  1. Resolves with rewarming of skin

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Related Studies

Ontology: Cutis marmorata (C0263401)

Concepts Disease or Syndrome (T047)
SnomedCT 201304006, 26825009
English Telangiectatica Congenita, cutis marmorata, Cutis marmorata (disorder), cutis; marmorata, marmorata; cutis, Cutis marmorata, Cutis Marmorata
Dutch cutis marmorata, cutis; marmorata, marmorata; cutis
French Cutis marmorata vascularis
German Cutis marmorata
Italian Cute marmorata
Portuguese Cutis marmorata
Spanish Cutis marmorata, piel marmórea (trastorno), piel marmórea
Japanese 大理石様皮膚, ダイリセキヨウヒフ
Czech Cutis marmorata
Hungarian Cutis marmorata