II. Epidemiology
- Incidence: 0.03% of newborns
III. Pathophysiology
- Congenital absence of skin
- Embryonic defect present in a small subset of patients
IV. Signs
- Bulla, ulceration or atrophic lesion
V. Distribution
- Most often at the scalp near the vertex
VII. Management
- Avoid secondary Bacterial Infection
- Surgical excision in some cases