II. Types
- Type 1: Primary Idiopathic Polymyositis (33%)
- Type 2: Primary Idiopathic Dermatomyositis (25%)
- Type 3: Neoplasia related
- Type 4: Childhood disease with Vasculitis
- Type 5: Collagen Vascular disease related
- Type 6: Miscellaneous (Inclusion body, Eosinophilic)
III. Diagnostic Criteria
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Dermatomyositis Diagnosis
- Four or more findings seen in Polymyositis (below)
- Cutaneous findings suggestive of Dermatomyositis
- Polymyositis Diagnosis (4 or more criteria below)
- Proximal Muscle Weakness (trunk, thighs, Shoulders)
- Increased serum Creatine Phosphokinase or Aldolase
- Muscle pain on grasping or spontaneously
- EMG myogenic changes (see Polymyositis Evaluation)
- Positive anti-Jo1 Antibody
- Nondestructive Arthritis or Arthralgia
- Pathologic inflammatory signs
- Systemic inflammation signs
- Temperature over 37 C at axilla
- C-Reactive Protein increased
- Erythrocyte Sedimentation Rate >20 mm/hour