II. Signs

  1. Periodic, repetitive and stereotypic limb movements (especially legs) during sleep
  2. Diagnosed as a disorder if the limb movements interfere with sleep to cause Daytime Somnolence or Fatigue
  3. Contrast with Restless Leg Syndrome which occurs prior to sleep

III. Diagnosis

  1. Diagnosis of exclusion once other Sleep Disorders are excluded (e.g. Sleep Apnea)
  2. Polysomnogram
    1. Adult: Periodic Limb Movement index >15/hour
    2. Child: Periodic Limb Movement index >5/hour

IV. Associated Conditions

  1. Restless Leg Syndrome (most with RLS have Periodic Limb Movements)
  2. REM Sleep Behavior Disorder
  3. Narcolepsy

V. Management

  1. Refer to sleep medicine

Images: Related links to external sites (from Bing)

Related Studies

Ontology: Nocturnal Myoclonus Syndrome (C0751774)

Definition (MSHCZE) Periodické pohyby končetinami ve spánku – porucha, při níž vznikají rytmické stereotypní pohyby obv. dolních končetin s častým probouzením a sníženou kvalitou spánku, druh dyssomnie. K tomuto stavu predisponuje řada celkových onemocnění (parkinsonismus, uremie, diabetes aj.), existuje vztah k syndromu neklidných nohou. Benigní hypnagogické záškuby jsou jednorázové, jen vzácně se opakující záškuby. Angl. periodic limb movements in sleep - PLMS. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ )
Definition (MSH) Excessive periodic leg movements during sleep that cause micro-arousals and interfere with the maintenance of sleep. This condition induces a state of relative sleep deprivation which manifests as excessive daytime hypersomnolence. The movements are characterized by repetitive contractions of the tibialis anterior muscle, extension of the toe, and intermittent flexion of the hip, knee and ankle. (Adams et al., Principles of Neurology, 6th ed, p387)
Concepts Disease or Syndrome (T047)
MSH D020189
ICD9 327.51
ICD10 G47.61
SnomedCT 418763003
Spanish trastorno de movimiento periódico de una extremidad (trastorno), trastorno de movimiento periódico de una extremidad, Trastorno periódico de movimiento de las extremidades, Síndrome de Mioclonía del Sueño, Síndrome de Mioclonía Nocturna, Trastorno del Movimiento Periódico del Sueño, Trastorno del Sueño de Movimiento Periódico, Trastorno de Movimiento Periódico de las Extremidades
Dutch Periodic Limb Movement Disorder, Periodic Limb Movement Disorder (PLMD), Myoclonussyndroom, nachtelijk, Nachtelijk myoclonussyndroom, Periodieke bewegingsstoornis, slaap, Periodieke extremiteitbewegingsstoornis, Slaapmyoclonussyndroom, Slaapstoornis, periodieke bewegingen, Syndroom, nachtelijk myoclonus-
French Trouble de mouvements périodiques des membres, Trouble de mouvements périodiques des membres (TMPM), Syndrome des myoclonies nocturnes, MPS (Mouvements Périodiques du Sommeil), Mouvements périodiques du sommeil, Myoclonies nocturnes, Syndrome des mouvements périodiques du sommeil, Syndrome des mouvements périodiques nocturnes des membres
German Periodische Bewegungen von Beinen und/oder Armen im Schlaf, PLMD, Myoklonie-Syndrom während des Schlafs, Nächtliches Myoklonie-Syndrom, Periodische Bewegungsstörungen während des Schlafs, Periodische Gliedmaßenbewegungen, Schlafstörung durch periodische Bewegungen
Italian Movimento periodico degli arti, Movimento periodico degli arti (PLMD), Disturbo da movimenti periodici nel sonno, Movimenti periodici delle gambe nel sonno, Sindrome da mioclono notturno, Disturbo da movimento periodico degli arti, Sindrome mioclonica notturna
Portuguese Afecção de movimentos periódicos dos membros, Síndrome da Mioclonia do Sono, Síndrome da Mioclonia Noturna, Transtorno do Movimento Periódico dos Membros, Transtorno do Movimento Periódico do Sono, Transtorno do Sono por Movimentos Periódicos
Japanese 周期性四肢運動障害(PLMD), シュウキセイシシウンドウショウガイ, シュウキセイシシウンドウショウガイPLMD, 運動障害-周期性四肢, 夜間ミオクローヌス症候群, 周期性四肢運動異常, 周期性四肢運動障害, 周期性運動性睡眠障害, 周期性運動障害-睡眠時, 四肢運動障害-周期性, 睡眠時ミオクローヌス症候群, 睡眠時周期性運動障害, 睡眠障害-周期性運動性
Swedish Sömnmyokloni
English PERIODIC LIMB MOVEMENT DIS, SLEEP RELAT PERIODIC LEG MOVEMENTS EXCESSIVE, EXCESSIVE PERIODIC SLEEP RELAT LEG MOVEMENTS, PERIODIC LEG MOVEMENTS EXCESSIVE SLEEP RELAT, PERIODIC MOVEMENT DIS SLEEP, SLEEP DIS PERIODIC MOVEMENTS, Periodic Limb Movement Disorder, Periodic Movement Disorder, Sleep, Sleep Disorder, Periodic Movements, Excessive Periodic Sleep-Related Leg Movements, Periodic Leg Movements, Excessive, Sleep-Related, Sleep-Related Periodic Leg Movements, Excessive, Myoclonus Syndrome, Nocturnal, Nocturnal Myoclonus Syndrome, Nocturnal Myoclonus Syndromes, Syndrome, Nocturnal Myoclonus, Myoclonus Syndrome, Sleep, Myoclonus Syndromes, Sleep, Sleep Myoclonus Syndrome, Sleep Myoclonus Syndromes, Syndrome, Sleep Myoclonus, Syndromes, Sleep Myoclonus, Periodic limb movement, Nocturnal Myoclonus Syndrome [Disease/Finding], disorder limb movement periodic, nocturnal myoclonus syndrome, periodic limb movement disorder, Sleep Related Periodic Leg Movements, Excessive, Excessive Periodic Sleep Related Leg Movements, Periodic limb movement disorder (PLMD), Periodic limb movement disorder, Periodic limb movement disorder (disorder)
Czech porucha spánku - periodické pohyby, spánkový myoklonický syndrom, Porucha periodického pohybu končetiny, noční myoklonický syndrom, periodické pohyby končetinami ve spánku
Finnish Yöllinen myoklonus -oireyhtymä
Russian MIOKLONUSA NOCHNOGO SINDROM, DVIZHENIIA PERIODICHESKIE VO VREMIA SNA, MIOKLONUSA SINDROM VO VREMIA SNA, ДВИЖЕНИЯ ПЕРИОДИЧЕСКИЕ ВО ВРЕМЯ СНА, МИОКЛОНУСА НОЧНОГО СИНДРОМ, МИОКЛОНУСА СИНДРОМ ВО ВРЕМЯ СНА
Polish Zespół miokloniczny nocny
Hungarian Periódikus végtagmozgás betegség, Periódikus végtagmozgás betegség (PLMD)
Norwegian Uttalte periodiske beinbevegelser under søvn, Uttalte søvnrelaterte periodiske benbevegelser, Søvnmyokloni, Uttalte søvnrelaterte periodiske beinbevegelser, Nattlig myokloni-syndrom, Uttalte periodiske benbevegelser under søvn