II. Causes: General
- See Congenital Heart Disease Causes
- Left heart obstructive disease
- Large shunt with pulmonary overflow
- Pump Failure
- Myocarditis (e.g. HH6, enterovirus, Parvovirus, Kawasaki's Disease)
- Cardiomyopathy
III. Causes: Age of presentation
- Week 1: Hypoplastic Left Heart Syndrome
- Week 2: Aortic Coarctation
- Week 4-12: Ventricular Septal Defect
- After Week 12: Valvular heart disease, Myocarditis
IV. Symptoms
- Poor feeding
- Diaphoresis with feeding
V. Signs
- See Congenital Heart Disease
- See Pediatric Murmur
- See Pediatric Vital Signs
- Biventricular failure is the rule
- S3 Heart Sound
- Tachypnea and other signs respiratory disease
- Tachycardia (out of proportion to condition)
- Hepatomegaly
- Pallor
VI. Labs
- Complete Blood Count (CBC)
- Brain Natriuretic Peptide (BNP or ntBNP)
- Venous Blood Gas
- Serum Lactate
- Thyroid Stimulating Hormone (TSH)
- Serum Troponin
- Increased in Myocarditis
- ALCAPA (Left Main Coronary Artery Disorder) can predispose to childhood Acute Coronary Syndrome
VII. Imaging
-
Chest XRay
- Pulmonary Edema
- Cardiomegaly
- Bedside Echocardiogram
- Decreased cardiac contractility
- Cardiac Tamponade
VIII. Diagnostics
- Electrocardiogram (EKG)
IX. Differential Diagnosis
- Neonatal Sepsis or Pediatric Sepsis
- Congenital metabolic conditions
- Acute Respiratory Distress Syndrome
X. Management
- Obtain Pediatric cardiology Consultation early in presentation
- Discuss acute stabilization management as high risk of decompensation
- Initiate transport to pediatric ICU facility with ECMO capability
-
General Measures
- Elevate head of bed 45 degrees
- Monitor Urine Output
- Improved Urine Output is a marker of effective Cardiogenic Shock management
- Specific evaluation if known cause
- See Congenital Heart Disease for General Measures and Complications
- Categorize the presentation
- Warm and Dry (goal, preserved perfusion without Pulmonary Edema)
- Warm and Wet (Preserved perfusion with Pulmonary Edema)
- Manageed with Diuretics and noninvasive Positive Pressure Ventilation
- Cold and Wet (Cardiogenic Shock with decreased perfusion and Pulmonary Edema)
- Requires additional inotropes and Vasopressors
- Cold and Dry (Severe Cardiogenic Shock)
- Requires Endotracheal Intubation and emergent cardiology evaluation and management
- References
- Claudius and Strobel (2024) EM:Rap, 9/9/2024
-
Supplemental Oxygen
- High Flow Oxygen indicated in non-Congenital Heart Disease cases
- Avoid hyperoxygenation in Congenital Heart Disease (risk of increased Pulmonary Edema)
- Adjust FIO2 to achieve Oxygen Saturation >90%
- Do not increase FiO2 in hypertrophic left heart
- Keep the ductus arteriosus patent
- Airway and Respiratory Support
- Non-Invasive Positive-pressure ventilation
- Endotracheal Intubation
- Early intubation for increasing respiratory distress, refractory to NIPPV (e.g. BiPap)
- Resolve Hypotension prior to Endotracheal Intubation (see below)
- Induction with Etomidate
- Avoid Ketamine due to risk of Dysrhythmia and increased Systemic Vascular Resistance
-
Hypotension
-
Vasopressors (Norepinephrine, Epinephrine, Dopamine)
- Start with small fluid boluses (if flat Jugular Vein or IVC Ultrasound for Volume Status)
- Epinephrine is a first line Vasopressor in Hypotension
- Vasopressors are contraindicated in ductal dependent systemic Blood Flow (i.e. Aortic Coarctation) as above
- Inotrope support (consult pediatric intensivist)
- Milrinone (preferred)
- Dobutamine (second-line alternative)
-
Vasopressors (Norepinephrine, Epinephrine, Dopamine)
-
Fluid Overload
- Furosemide (Lasix) 1-2 mg/kg IV
-
Exercise caution with Nitroglycerin (discuss first with cardiology)
- Many CHD patients are Preload dependent and may have catastrophic drop in Blood Pressure with nitrates
- Analgesia and sedation
- Sedation with Morphine Sulfate 0.05 to 0.1 mg/kg IV
- Fluid maintenance
- Fluids to 66% of expected fluid maintenance requirement
XI. References
- Herndon (2003) AAFP Board Review, Seattle
- Claudius, Behar, Salway and Kearl in Herbert (2018) EM:Rap 18(5): 1-3
- Claudius and Kallay in Swadron (2023) EM:Rap 23(2): 6-7