II. Causes: General
- See Congenital Heart Disease Causes
- Left heart obstructive disease
- Large shunt with pulmonary overflow
- Pump Failure- Myocarditis (e.g. HH6, Enterovirus, Parvovirus, Kawasaki's Disease)
- Cardiomyopathy
 
III. Causes: Age of presentation
- Week 1: Hypoplastic Left Heart Syndrome
- Week 2: Aortic Coarctation
- Week 4-12: Ventricular Septal Defect
- After Week 12: Valvular heart disease, Myocarditis
IV. Symptoms
- Poor feeding
- Diaphoresis with feeding
V. Signs
- See Congenital Heart Disease
- See Pediatric Murmur
- See Pediatric Vital Signs
- Biventricular failure is the rule
- S3 Heart Sound
- Tachypnea and other signs respiratory disease
- Tachycardia (out of proportion to condition)
- Hepatomegaly
- Pallor
VI. Labs
- Complete Blood Count (CBC)
- Brain Natriuretic Peptide (BNP or ntBNP)
- Venous Blood Gas
- Serum Lactate
- Thyroid Stimulating Hormone (TSH)
- Serum Troponin- Increased in Myocarditis
- ALCAPA (Left Main Coronary Artery Disorder) can predispose to childhood Acute Coronary Syndrome
 
VII. Imaging
- 
                          Chest XRay
                          - Pulmonary Edema
- Cardiomegaly
 
- Bedside Echocardiogram- Decreased cardiac contractility
- Cardiac Tamponade
 
VIII. Diagnostics
- Electrocardiogram (EKG)
IX. Differential Diagnosis
- Neonatal Sepsis or Pediatric Sepsis
- Congenital metabolic conditions
- Acute Respiratory Distress Syndrome
X. Management
- Obtain Pediatric cardiology Consultation early in presentation- Discuss acute stabilization management as high risk of decompensation
- Initiate transport to pediatric ICU facility with ECMO capability
 
- 
                          General Measures- Elevate head of bed 45 degrees
- Monitor Urine Output- Improved Urine Output is a marker of effective Cardiogenic Shock management
 
- Specific evaluation if known cause- See Congenital Heart Disease for General Measures and Complications
 
- Categorize the presentation- Warm and Dry (goal, preserved perfusion without Pulmonary Edema)
- Warm and Wet (Preserved perfusion with Pulmonary Edema)- Manageed with Diuretics and noninvasive Positive Pressure Ventilation
 
- Cold and Wet (Cardiogenic Shock with decreased perfusion and Pulmonary Edema)- Requires additional inotropes and Vasopressors
 
- Cold and Dry (Severe Cardiogenic Shock)- Requires Endotracheal Intubation and emergent cardiology evaluation and management
 
- References- Claudius and Strobel (2024) EM:Rap, 9/9/2024
 
 
 
- 
                          Supplemental Oxygen
                          - High Flow Oxygen indicated in non-Congenital Heart Disease cases
- Avoid hyperoxygenation in Congenital Heart Disease (risk of increased Pulmonary Edema)- Adjust FIO2 to achieve Oxygen Saturation >90%
- Do not increase FiO2 in hypertrophic left heart- Keep the ductus arteriosus patent
 
 
 
- Airway and Respiratory Support- Non-Invasive Positive-pressure ventilation
- Endotracheal Intubation- Early intubation for increasing respiratory distress, refractory to NIPPV (e.g. BiPap)
- Resolve Hypotension prior to Endotracheal Intubation (see below)
- Induction with Etomidate- Avoid Ketamine due to risk of Dysrhythmia and increased Systemic Vascular Resistance
 
 
 
- 
                          Hypotension
                          - 
                              Vasopressors (Norepinephrine, Epinephrine, Dopamine)- Start with small fluid boluses (if flat Jugular Vein or IVC Ultrasound for Volume Status)
- Epinephrine is a first line Vasopressor in Hypotension
- Vasopressors are contraindicated in ductal dependent systemic Blood Flow (i.e. Aortic Coarctation) as above
 
- Inotrope support (consult pediatric intensivist)- Milrinone (preferred)
- Dobutamine (second-line alternative)
 
 
- 
                              Vasopressors (Norepinephrine, Epinephrine, Dopamine)
- 
                          Fluid Overload
                          - Furosemide (Lasix) 1-2 mg/kg IV
- 
                              Exercise caution with Nitroglycerin (discuss first with cardiology)- Many CHD patients are Preload dependent and may have catastrophic drop in Blood Pressure with nitrates
 
 
- Analgesia and sedation- Sedation with Morphine Sulfate 0.05 to 0.1 mg/kg IV
 
- Fluid maintenance- Fluids to 66% of expected fluid maintenance requirement
 
XI. References
- Herndon (2003) AAFP Board Review, Seattle
- Claudius, Behar, Salway and Kearl in Herbert (2018) EM:Rap 18(5): 1-3
- Claudius and Kallay in Swadron (2023) EM:Rap 23(2): 6-7
