Definition (MSH)
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A congenital anomaly caused by the failed development of TRUNCUS ARTERIOSUS into separate AORTA and PULMONARY ARTERY. It is characterized by a single arterial trunk that forms the outlet for both HEART VENTRICLES and gives rise to the systemic, pulmonary, and coronary arteries. It is always accompanied by a ventricular septal defect.
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Definition (NCI)
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A rare congenital cardiovascular disorder characterized by the failure of the embryologic structure truncus arteriosus to divide into the aorta and pulmonary trunk. It results in the presence of a single vessel instead of two vessels leading out of the heart. Clinical signs and symptoms include cyanosis that is present at birth, poor growth, dyspnea, tachypnea, arrhythmia, cardiomegaly, and heart failure. If it is not surgically repaired, it leads to death.
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Concepts |
Congenital Abnormality
(T019)
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MSH |
D014339
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ICD9 |
745.0 |
ICD10 |
Q20.0
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SnomedCT |
61959006, 204292000, 394525006, 204294004, 204291007 |
English |
Truncus Arteriosus, Persistent, CAT - Common arterial trunk, Common arterial trunk, Common aortopulmon trunk NOS, Common aortopulmonary trunk NOS, Persistent Truncus Arteriosus, common truncus arteriosis, common truncus arteriosis (diagnosis), Truncus arteriosus persistent, PERSISTENT TRUNCUS ARTERIOSUS, PTA, Truncus Arteriosus, Persistent [Disease/Finding], Common truncus arteriosus, Common arterial trunk (truncus arteriosus), Truncus Arteriosus, common arterial trunk (diagnosis), Persistent truncus arteriosus (disorder), Truncus arteriosus, Common aortopulmonary trunk NOS (disorder), Common aorto-pulmonary trunk, TA - Truncus arteriosus, Truncus arteriosus, Persistent, Common Truncus Arteriosus, Persistent truncus arteriosus, Common aortopulmonary trunk, Truncus arteriosus communis, Common truncus arteriosus (disorder), common; arterial trunk, common; truncus, truncus; arteriosus, truncus; common, arteriosus; truncus, artery; common trunk, Common truncus, Absent septum between aorta and pulmonary artery |
Dutch |
truncus arteriosus communis, gewone truncus, arterie; truncus gemeenschappelijk, arteriosus; truncus, gemeenschappelijk; arteriële truncus, gemeenschappelijk; truncus, truncus; arteriosus, truncus; gemeenschappelijk, persisterende truncus arteriosus, Persistente truncus arteriosus, Truncus arteriosus, persistente, Gemeenschappelijke arteriële truncus |
French |
Tronc commun, TAC (Tronc Artériel Commun), Persistance du tronc artériel, Tronc artériel commun |
German |
Truncus arteriosus communis, persistierender Truncus arteriosus, Persistierender Truncus arteriosus, Truncus arteriosus communis persistens, Truncus arteriosus, persistierender |
Italian |
Tronco comune, Tronco arterioso comune, Tronco arterioso persistente |
Portuguese |
Tronco comum, Tronco arterial comum, Persistência do Tronco Arterioso, Persistência do tronco arterial, Persistência do Tronco Arterial |
Spanish |
Tronco común, Tronco arterioso común, tronco arterioso persistente (trastorno), tronco arterial común (tronco arterioso), tronco arterioso persistente, tronco arterioso común (trastorno), tronco aortopulmonar común, SAI, tronco aortopulmonar común, SAI (trastorno), Tronco Arterioso Persistente, tronco aortopulmonar común, tronco arterioso común, Tronco arterioso persistente, Tronco Arterial Persistente |
Japanese |
ソウドウミャクカンイザン, ソウドウミャクカンショウ, 総動脈幹症, 遺残-総動脈幹, 動脈幹遺残, 総動脈幹遺残, 総動脈幹遺残症, 総動脈幹開存, 総動脈幹開存症, 総動脈幹残遺, 遺残-動脈幹 |
Czech |
truncus arteriosus persistens, Společný truncus, Truncus arteriosus communis, Perzistující truncus arteriosus |
Finnish |
Yhteinen valtimorunko
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Russian |
PERSISTIRUIUSHCHII ARTERIAL'NYI STVOL, ARTERIAL'NYI STVOL OBSHCHII, АРТЕРИАЛЬНЫЙ СТВОЛ ОБЩИЙ, ПЕРСИСТИРУЮЩИЙ АРТЕРИАЛЬНЫЙ СТВОЛ |
Korean |
총동맥줄기
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Swedish |
Truncus arteriosus, persisterande
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Polish |
Pień tętniczy przetrwały
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Hungarian |
Truncus arteriosus ((communis)), Persistáló truncus arteriosus, Common truncus |
Norwegian |
Persisterende truncus arteriosus
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