Definition (MSHCZE)
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Soubor příznaků vrozené srdeční vady, při které se defekt komorového septa (VSD) sdružuje s dextropozicí aorty (nasedá nad defektem). Vada je cyanotická a označuje se někdy jako prostá transpozice s nasedající aortou. Plný obraz klasické Eisenmengerovy tetralogie se objeví po rozvoji plicní hypertenze s hypertrofií pravé komory a obrácením zkratu. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ )
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Definition (NCI)
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A syndrome characterized by the reversal of a septal defect-associated left-to-right shunt due to the resulting secondary pulmonary hypertension. The presence of the pulmonary hypertension causes increased pressure in the right heart chambers resulting in the reversal of the shunt into a right-to-left shunt. Signs and symptoms include cyanosis, pulmonary hypertension, heart failure, and high red blood cell count.
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Definition (MSH)
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A condition associated with VENTRICULAR SEPTAL DEFECT and other congenital heart defects that allow the mixing of pulmonary and systemic circulation, increase blood flow into the lung, and subsequent responses to low oxygen in blood. This complex is characterized by progressive PULMONARY HYPERTENSION; HYPERTROPHY of the RIGHT VENTRICLE; CYANOSIS; and ERYTHROCYTOSIS.
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Concepts |
Disease or Syndrome
(T047)
, Congenital Abnormality
(T019)
|
MSH |
D004541
|
ICD10 |
I27.89
, Q21.8 |
SnomedCT |
83130006, 445928005, 204311009, 270547008, 156914003 |
English |
Complex, Eisenmenger, Eisenmenger Complex, Eisenmenger Syndrome, Eisenmenger's Complex, Eisenmenger's Syndrome, Eisenmengers Complex, Eisenmengers Syndrome, Syndrome, Eisenmenger, Complex, Eisenmenger's, Syndrome, Eisenmenger's, Eisenmenger's syndrome (diagnosis), Eisenmenger defect, Eisenmenger Complex [Disease/Finding], eisenmenger syndrome, eisenmenger's complex, eisenmenger's syndrome, eisenmengers complex, eisenmenger complex, eisenmengers syndrome, Eisenmenger's syndrome (disorder), Eisenmenger complex, Eisenmenger's syndrome, Eisenmenger's complex, Eisenmenger syndrome, Eisenmenger's complex (disorder), Eisenmenger's defect, Eisenmenger's defect (disorder), Eisenmenger; complex, Eisenmenger; defect, Eisenmenger, complex; Eisenmenger, defect; Eisenmenger, Eisenmenger's defect or complex |
Swedish |
Eisenmengers komplex
|
Japanese |
アイゼンメンゲルショウコウグン, Eisenmenger症候群, Eisenmenger複合, アイゼンメンゲルコンプレックス, アイゼンメンゲル症候群, アイゼンメンゲル複合, アイゼンメンガー複合体 |
Finnish |
Eisenmengerin oireyhtymä
|
Russian |
EIZENMENGERA SINDROM, EIZENMENGERA KOMPLEKS, ЭЙЗЕНМЕНГЕРА КОМПЛЕКС, ЭЙЗЕНМЕНГЕРА СИНДРОМ |
Italian |
Sindrome di Eisenmenger, Complesso di Eisenmenger |
Polish |
Zespół Eisenmengera
|
Spanish |
complejo de Eisenmenger, síndrome de Eisenmenger, síndrome de Eisenmenger (trastorno), complejo de Eisenmenger (trastorno), defecto de Eisenmenger (trastorno), defecto de Eisenmenger, Complejo de Eisenmenger, Síndrome de Eisenmenger |
Hungarian |
Eisenmenger-syndroma
|
Norwegian |
Eisenmengers syndrom
|
Czech |
plicní vaskulární nemoc, Eisenmengerův komplex, Eisenmengerův syndrom |
Dutch |
Eisenmenger; complex, Eisenmenger; defect, complex; Eisenmenger, defect; Eisenmenger, Eisenmenger-complex, Eisenmenger-syndroom, Syndroom, Eisenmenger- |
Portuguese |
Síndroma de Eisenmenger, Complexo de Eisenmenger, Síndrome de Eisenmenger |
French |
Syndrome d'Eisenmenger, Complexe d'Eisenmenger |
German |
Eisenmenger-Komplex, Eisenmenger-Syndrom |