II. Epidemiology
-
Incidence
- Occurs in up to 10 to 22% of Cystic Fibrosis patients
III. Mechanism
- Small Bowel Obstruction in the ileocecal region in Cystic Fibrosis patients
- Triggered by pancreatic insufficiency, dysmotility and Dehydration
IV. Findings
- Presents with Right lower quadrant mass
V. Differential Diagnosis
- Constipation
- Other Small Bowel Obstruction
- Volvulus
- Intussception
- Fibrosing Colonopathy
- Appendicitis
- Crohns Disease
- Malignancy
VI. Imaging
-
CT Abdomen (first line study)
- Diagnostic for Distal Intestinal Obstruction
- Evaluates differential diagnosis
- Abdominal XRay
- Demonstrates obstructive findings, but CT Abdomen is typically required
VII. Management
- Incomplete Obstruction
- Nonsurgical management
- Oral rehydration
- Enemas, Osmotic Laxatives and Stool Softeners
- Consider osmotic contrast
- Complete Obstruction
- Nasogastric Tube decompression
- Laparotomy with manual decompression of obstruction
VIII. Complications
- Intestinal Ischemia
- Bowel perforation
IX. References
- Uddin and Crawford (2023) Crit Dec Emerg Med 37(9): 15-5
- Colombo (2011) J Cyst Fibros 10(suppl 2): 524-8 [PubMed]
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Related Studies
Concepts | Disease or Syndrome (T047) |
ICD10 | E84.19 |
SnomedCT | 233662009 |
English | DIOS-Dist intest obstr syndrom, Dist intest obstr syndrome, MIE - Meconium ileus equiv, Meconium ileus equivalent syndrome, DIOS - Distal intestinal obstruction syndrome, Distal intestinal obstruction syndrome, MIE - Meconium ileus equivalent, Meconium ileus equivalent, Distal intestinal obstruction syndrome (disorder) |
Italian | Sindrome da ostruzione distale dell'intestino, Sindrome equivalente dell'ileo da meconio |
Dutch | meconiumileus equivalent-syndroom, distaal intestinaal obstructiesyndroom |
German | Meconium ileus-artiges Syndrom, Distales intestinales Obstruktionssyndrom |
Portuguese | Síndrome equivalente a íleus meconial, Síndrome de obstrução intestinal distal |
Spanish | Síndrome semejante al íleo meconial, síndrome de obstrucción intestinal distal (trastorno), síndrome de obstrucción intestinal distal, Síndrome de obstrucción intestinal distal |
Japanese | 胎便イレウス様症候群, 末端腸閉塞症候群, タイベンイレウスヨウショウコウグン, マッタンチョウヘイソクショウコウグン |
French | Syndrome équivalent de l'iléus méconial, Syndrome d'obstruction de l'intestin distal |
Czech | Syndrom distální střevní obstrukce, Syndrom odpovídající mekoniovému ileu |
Hungarian | Meconium ileus equivalens syndroma, Intestinalis distalis obstructio syndroma |