Definition (NCI)
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A progressive motor neuron disorder affecting the muscles which are innervated by cranial nerves of the lower brain stem. Signs and symptoms include difficulties in chewing and swallowing, dysarthria, and weakness of the facial muscles and tongue.
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Definition (MSH)
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A motor neuron disease marked by progressive weakness of the muscles innervated by cranial nerves of the lower brain stem. Clinical manifestations include dysarthria, dysphagia, facial weakness, tongue weakness, and fasciculations of the tongue and facial muscles. The adult form of the disease is marked initially by bulbar weakness which progresses to involve motor neurons throughout the neuroaxis. Eventually this condition may become indistinguishable from AMYOTROPHIC LATERAL SCLEROSIS. Fazio-Londe syndrome is an inherited form of this illness which occurs in children and young adults. (Adams et al., Principles of Neurology, 6th ed, p1091; Brain 1992 Dec;115(Pt 6):1889-1900)
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Concepts |
Disease or Syndrome
(T047)
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MSH |
D010244
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ICD9 |
335.22 |
ICD10 |
G12.22
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SnomedCT |
230547002, 54304004 |
English |
Bulbar Palsies, Bulbar Palsy, Bulbar Paralyses, Bulbar Paralysis, Palsies, Bulbar, Paralysis, Bulbar, BULBAR PALSY, PARALYSIS BULBAR, Palsy, Bulbar, Bulbar palsies, progressive bulbar palsy (diagnosis), progressive bulbar palsy, Paralysis bulbar, Bulbar Palsies, Progressive, Bulbar Palsy, Progressive, Palsies, Progressive Bulbar, Palsy, Progressive Bulbar, Progressive Bulbar Palsies, Progressive Bulbar Palsy, Bulbar Palsy, Progressive [Disease/Finding], bulbar palsies, bulbar palsy progressive, bulbar palsy, bulbar paralysis, Bulbar palsy (disorder), Progressive bulbar palsy, PBP - Progressive bulbar palsy, Bulbar palsy, Bulbar paralysis, Progressive bulbar palsy (disorder), bulbar; paralysis, paralysis; bulbar |
French |
PARALYSIE BULBAIRE, Paralysie bulbaire, Paralysie bulbaire progressive |
Portuguese |
PARALISIA BULBAR, Paresia Bulbar Progressiva, Paralisia bulbar, Paralisia progressiva bulbar, Paralisia Bulbar, Paralisia Bulbar Progressiva |
Spanish |
PARALISIS BULBAR, Paresia Bulbar Progresiva, parálisis bulbar progresiva (trastorno), parálisis bulbar progresiva, parálisis bulbar, Parálisis bulbar progresiva, Parálisis bulbar, Parálisis Bulbar Progresiva, Parálisis Bulbar |
Dutch |
paralyse bulbair, bulbaire paralyse, bulbair; paralyse, paralyse; bulbair, bulbaire verlamming, progressieve bulbairparalyse, Bulbaire paralyse, progressieve, Bulbaire progressieve paralyse, Paralyse, bulbaire, Paralyse, bulbaire progressieve, Progressieve bulbaire paralyse |
German |
Paralyse bulbaer, Bulbaer-Paralyse, BULBAERPARALYSE (DURCH ISCHAEMIE), BULBAERPARALYSE, Bulbaerparalyse, progressive Bulbaerparalyse, Bulbärparalyse, Bulbärparalyse, progressive, Paralyse, Bulbär- |
Swedish |
Bulbär pares, progressiv
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Japanese |
シンコウセイキュウマヒ, キュウマヒ, 延髄球不全麻痺, 延髄不全麻痺, ファチオ-ロンデ症候群, 進行性球麻痺, 麻痺-延髄, ファチオ-ロンデ病, ファチオ-ロンド症候群, ファチオ-ロンデ萎縮, 麻痺-球, ファチオ-ロンド病, ファチオ-ロンド萎縮, 延髄麻痺, 球麻痺-進行性, 延髄球麻痺, Fazio-Londe病, 球麻痺 |
Czech |
paralýza bulbární, bulbární obrna progresivní, Bulbární paralýza, Bulbární progresivní obrna, Bulbární obrna |
Finnish |
Etenevä bulbaariparalyysi
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Russian |
PARALICH BUL'BARNYI, BUL'BARNYI PARALICH PROGRESSIVNYI, BUL'BARNYI PARALICH, PARALICH BUL'BARNYI PROGRESSIVNYI, БУЛЬБАРНЫЙ ПАРАЛИЧ, БУЛЬБАРНЫЙ ПАРАЛИЧ ПРОГРЕССИВНЫЙ, ПАРАЛИЧ БУЛЬБАРНЫЙ, ПАРАЛИЧ БУЛЬБАРНЫЙ ПРОГРЕССИВНЫЙ |
Italian |
Paralisi bulbare, Paralisi bulbare progressiva |
Polish |
Porażenie opuszkowe postępujące, Porażenie opuszkowe, Zespół Fazio-Londe |
Hungarian |
Progressiv bulbaris bénulás, Bulbaris paralysis, Bulbaris paresis, Paralysis bulbaris |
Norwegian |
Progressiv bulbærparese
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