Definition (NCI)
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A chronic autoimmune disorder characterized by the development of blisters and ulcers in mucous membranes. It affects most often the gums, eyelids and genital mucosa sites.
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Definition (MSH)
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A chronic blistering disease with predilection for mucous membranes and less frequently the skin, and with a tendency to scarring. It is sometimes called ocular pemphigoid because of conjunctival mucous membrane involvement.
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Concepts |
Disease or Syndrome
(T047)
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MSH |
D010390
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ICD9 |
694.6 |
ICD10 |
L12.1
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SnomedCT |
200915000, 200913007, 34250006 |
English |
Benign Mucous Membrane Pemphigoid, Pemphigoid, Benign Mucous Membrane, Pemphigoid, Cicatricial, Mucous Membrane Pemphigoid, Benign, Cicatricial Pemphigoid, Benign mm pemphigoid NOS, Benign mucous membrane pemphigoid NOS, mucosynechial atrophic bullous dermatitis, cicatricial pemphigoid (diagnosis), mucosynechial atrophic bullous dermatitis (diagnosis), cicatricial pemphigoid, Pemphigoid, Benign Mucous Membrane [Disease/Finding], Benign Mucosal Pemphigoids, Mucosal Pemphigoids, Benign, Pemphigoid, Benign Mucosal, Benign Mucosal Pemphigoid, Mucosal Pemphigoid, Benign, Pemphigoids, Benign Mucosal, mucosal pemphigoid benign, mucous membrane pemphigoid, benign membrane mucous pemphigoid, Benign mucous membrane pemphigoid NOS (disorder), Cicatricial pemphigoid, Benign mucous membrane pemphigoid, Mucosynechia atrophic bullous dermatitis, Benign mucosal pemphigoid, Mucous membrane pemphigoid, Scarring pemphigoid, Benign mucous membrane pemphigoid (disorder), bullous; eczema, mucosynechial, atrophic, cicatricial; pemphigoid, eczema; bullous, mucosynechial, atrophic, pemphigoid; cicatricial, scar; pemphigoid, Mucosynechial atrophic bullous dermatitis |
Dutch |
cicatriciaal pemfigoïd, benigne slijmvliezenpemfigoïd, bulleus; eczeem, mucosynechiaal, atrofisch, cicatricieel; pemfigoïd, eczeem; bulleus, bullosa, mucosynechiaal, atrofisch, litteken; pemfigoïd, pemfigoïd; cicatricieel, Cicatricieel pemfigoïd, Muceusmembraanpemfigoïd, benigne, Pemfigoïd, cicatricieel |
German |
vernarbendes Pemphigoid, gutartiges Schleimhautpemphigoid, Vernarbendes Pemphigoid, Pemphigoid, benignes Schleimhaut-, Pemphigoid, narbenbildendes |
Italian |
Pemfigoide benigno delle mucose, Pemfigoide cicatriziale, Pemfigoide benigno mucomembranoso |
Portuguese |
Penfigóide benigno das membranas, Penfigóide cicatricial, Penfigoide Mucomembranoso Benigno, Penfigoide Cicatricial, Penfigoide Benigno de Mucosa, Penfigoide Benigno da Membrana Mucosa |
Spanish |
Penfigoide benigno de la membrana mucosa, Pénfigo cicatricial, penfigoide benigno de las membranas mucosas, penfigoide benigno de las membranas mucosas (trastorno), dermatitis ampollosa mucosinequial atrófica, penfigoide benigno de membranas mucosas (trastorno), penfigoide benigno de membranas mucosas, penfigoide cicatricial, penfigoide cicatrizal, penfigoide mucoso benigno, Penfigoide Benigno de la Membrana Mucosa, Penfigoide Cicatricial |
Swedish |
Pemfigoid, slemhinna, benign
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Japanese |
ハンコンセイルイテンポウソウ, リョウセイネンマクルイテンポウソウ, 瘢痕性類天疱瘡, 類天疱瘡-良性粘膜性, 良性粘膜型類天疱瘡, 良性粘膜性類天疱瘡, 良性粘膜類天疱瘡, 類天疱瘡-瘢痕性, 類天疱瘡-良性粘膜型 |
Czech |
pemfigoid sliznice benigní, Benigní pemfigoid sliznice, Jizvící pemfigoid |
Finnish |
Hyvänlaatuinen limakalvopemfigoidi
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Russian |
PEMFIGOID RUBTSOVYI, PEMFIGOID DOBROKACHESTVENNYI SLIZISTYKH OBOLOCHEK, ПЕМФИГОИД ДОБРОКАЧЕСТВЕННЫЙ СЛИЗИСТЫХ ОБОЛОЧЕК, ПЕМФИГОИД РУБЦОВЫЙ |
Korean |
흉터성 유사천포창
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Polish |
Pemfigoid śluzówkowy łagodny, Pemfigoid błon śluzowych łagodny |
Hungarian |
Heges pemphigoid, Benignus nyálkahártya pemphigoid |
Norwegian |
Slimhinnepemfigoid, benign, Benign mucosapemfigoid, Benign slimhinnepemfigoid, Pemfigoid, arrdannende, Arrdannende pemfigoid, Benign mukosal pemfigoid, Cicatrisiell pemfigoid, Pemfigoid, cicatrisiell |
French |
Conjonctivite mucosynéchiante, Dermatite mucosynéchiante de Lortat-Jacob, Pemphigoïde bénigne des muqueuses, Pemphigoïde cicatricielle, Pemphigus oculaire |