Definition (MSH)
|
Autoimmune disease characterized by subepidermal blisters and linear deposition of autoantibodies at the dermoepidermal junction. The accumulated autoantibodies are of IMMUNOGLOBULIN A and occasionally IMMUNOGLOBULIN G classes against epidermal BASEMENT MEMBRANE proteins. The dermatosis is sometimes associated with malignancies and use of certain drugs (e.g., VANCOMYCIN).
|
Concepts |
Disease or Syndrome
(T047)
|
MSH |
D062027
|
SnomedCT |
95330001
|
English |
Linear IgA bullous dermatosis, linear IgA dermatoses (diagnosis), linear IgA dermatoses, linear IgA dermatosis, Linear Ig A disease, Linear IgA, linear iga bullous dermatosis, dermatosis iga linear, linear iga, linear iga disease, linear iga dermatosis, IgA Dermatoses, Linear, Linear IgA Dermatoses, Linear IgA Bullous Dermatosis, Linear IgA Dermatosis, Dermatosis, Linear IgA, IgA Dermatosis, Linear, Dermatoses, Linear IgA, Linear IgA Bullous Dermatosis [Disease/Finding], Linear immunoglobulin A dermatosis (disorder), Linear IgA dermatosis (disorder), Linear immunoglobulin A dermatosis, IgA - Linear immunoglobulin A bullous dermatosis, LAD - Linear IgA disease, Linear IgA dermatosis, Linear IgA disease, Linear immunoglobulin A bullous dermatosis |
Dutch |
lineaire IgA bulleuze dermatose, lineaire IgA, lineaire IgA ziekte |
French |
IgA linéaire, Dermatose à IgA linéaire, Dermatose bulleuse linéaire à IgA, Dermatose linéaire à IgA, Dermatose bulleuse à dépôts linéaires d'IgA, Dermatose à dépôts linéaires d'IgA, Dermatose bulleuse à IgA linéaire, Maladie par dépôts linéaires d'IgA |
German |
lineare blasenbildende IgA-Dermatose, lineare IgA, Lineare IgA-Dermatose, lineare IgA-Erkrankung |
Portuguese |
IgA linear, Dermatose bolhosa IgA linear, Dermatose Linear Bolhosa por IgA, Dermatose Bolhosa Linear por IgA, Doença IgA linear |
Spanish |
IgA lineal, Dermatosis bullosa linear mediada por IgA, Dermatosis Bullosa IgA Lineal, dermatosis lineal por inmunoglobulina A, dermatosis lineal por IgA, dermatosis lineal por inmunoglobulina A (trastorno), Enfermedad de la IgA lineal |
Japanese |
リニアIgA, リニアIgA水疱性皮膚症, リニアIgA病, リニアIgAスイホウセイヒフショウ, リニアIgAビョウ, リニアIgA |
Czech |
Lineární IgA, Lineární IgA choroba, Lineární IgA bulózní dermatóza, LABD, lineární IgA dermatóza, lineární IgA bulózní dermatóza |
Italian |
Malattia da IgA lineari, IgA lineari, Dermatosi bollosa da IgA lineari, Dermatosi bollosa a IgA lineari |
Hungarian |
Linearis Ig A betegség, Lineáris IgA, Lineáris Ig A betegség, Lineáris Ig A bullosus dermatosis |
Polish |
Dermatoza pęcherzowa linijna IgA, Linijna dermatoza pęcherzowa, Dermatoza pęcherzowa z linijnym odkładaniem IgA |
Russian |
ЛЕКАРСТВОМ ИНДУЦИРОВАННЫЙ ЛИНЕЙНЫЙ IGA-БУЛЛЕЗНЫЙ ДЕРМАТОЗ, ДЕРМАТОЗ ЛИНЕЙНЫЙ IGA/IGG, DERMATOZ LINEINYI IGA/IGG, LEKARSTVOM INDUTSIROVANNYI LINEINYI IGA-BULLEZNYI DERMATOZ, KHRONICHESKOE BULLEZNOE ZABOLEVANIE U DETEI, ЛИНЕЙНЫЙ IGA-ЗАВИСИМЫЙ БУЛЛЕЗНЫЙ ДЕРМАТОЗ, ХРОНИЧЕСКОЕ БУЛЛЕЗНОЕ ЗАБОЛЕВАНИЕ У ДЕТЕЙ, LINEINYI IGA-ZAVISIMYI BULLEZNYI DERMATOZ, ЛИНЕЙНЫЙ IGA БУЛЛЕЗНЫЙ ДЕРМАТОЗ, LINEINYI IGA BULLEZNYI DERMATOZ |
Norwegian |
Lineær IgA bulløs dermatose
|