II. Definition
- Less common, milder and superficial form of Pemphigus
III. Signs
- Onset on skin of face in butterfly distribution
- May also involve scalp, chest or upper back
- Rarely involves Oral Mucosa
- Nikolsky's Sign absent
IV. Variants
- Pemphigus erythematosus (Senear-Usher Syndrome)
- Localized variant of Pemphigus Foliaceus
- Associated with Systemic Lupus Erythematosus
- Antinuclear Antibody positive
- Fogo selvagem
- Variant of Pemphigus Foliaceus
- Endemic to Brasil and Colombia
- Associated with chronic Black Fly exposure
- Pemphigus herpetiformis
- Pruritic Blister formation
- May appear similar to Dermatitis Herpetiformis
-
Drug-Induced Pemphigus
- Associated with Penicillamine and Captopril
- Differentiate from Drug-Triggered Pemphigus
- Unmasks Pemphigus Vulgaris
V. Labs: Histology
- Blister forms just below Stratum Corneum of Epidermis
VI. References
- Habif (1996) Clinical Dermatology, Mosby, p. 510
- Cotell (2000) Am J Emerg Med 18(3):288-99 [PubMed]
Images: Related links to external sites (from Bing)
Related Studies
| Concepts | Disease or Syndrome (T047) |
| ICD10 | L10.4 |
| SnomedCT | 36739006 |
| Dutch | erythemateuze pemphigus, pemphigus erythematosus, erythematosus; pemphigus, pemphigus; erythematosus, Pemphigus erythematosus |
| French | Pemphigus érythémateux |
| German | Pemphigus erythematoes, Pemphigus erythematosus |
| Italian | Pemfigo eritematoso |
| Portuguese | Pênfigo eritematoso |
| Spanish | Pénfigo eritematoso, pénfigo eritematoso (trastorno), pénfigo eritematoso, síndrome de Senear - Usher |
| Japanese | 紅斑性天疱瘡, ｺｳﾊﾝｾｲﾃﾝﾎﾟｳｿｳ |
| English | pemphigus erythematosus (diagnosis), pemphigus erythematosus, Pemphigus erythematous, Pemphigus erythematosis, Pemphigus erythematosus, Senear-Usher syndrome, Pemphigus erythematosus (disorder), Senear-Usher, Usher-Senear, erythematosus; pemphigus, pemphigus; erythematosus, Pemphigus, erythematosus |
| Czech | Pemphigus erythematosus, Erytematózní pemfigus, pemphigus erythematosus |
| Korean | 홍반성 천포창 |
| Hungarian | Pemphigus erythematosis, Pemphigus erythemas, Pemphigus erythematosus |
Ontology: Pemphigus Foliaceus (C0263313)
| Concepts | Disease or Syndrome (T047) |
| MSH | D010392 |
| ICD10 | L10.2 |
| SnomedCT | 35154004 |
| Dutch | pemphigus foliaceus, foliaceus; pemphigus, pemphigus; foliaceus, Pemphigus foliaceus |
| French | Pemphigus foliaceus, Pemphigus foliacé |
| German | Pemphigus blattfoermig, Pemphigus foliaceus |
| Italian | Pemfigo foliaceo, Pemfigo fogliaceo |
| Portuguese | Pênfigo foliáceo |
| Spanish | Pénfigo foliáceo, pénfigo foliáceo (trastorno), pénfigo foliáceo |
| Japanese | 落葉状天疱瘡, ﾗｸﾖｳｼﾞｮｳﾃﾝﾎﾟｳｿｳ |
| English | pemphigus foliaceus (diagnosis), pemphigus foliaceus, pemphigus foliaceous, Pemphigus foliaceus, Pemphigus foliaceous, PF - Pemphigus foliaceous, Pemphigus foliaceus (disorder), foliaceous; pemphigus, Cazenave, pemphigus; foliaceous, Pemphigus, foliaceus, Foliaceus, Pemphigus, Pemphigus Foliaceus |
| Czech | Pemphigus foliaceus |
| Korean | 낙엽상 천포창 |
| Hungarian | Pemphigus foliaceus, foliaceus pemphigus |
| Norwegian | Pemphigus foliaceus |
Ontology: Pemphigus and fogo selvagem (C0263314)
| Concepts | Disease or Syndrome (T047) |
| MSH | C535551 |
| ICD10 | L10.3 |
| SnomedCT | 200906007, 46459009 |
| English | Brazilian pemphigus [fogo selvagem], Brazilian pemphigus foliaceus (diagnosis), fogo selvagem, Endemic pemphigus foliaceus, Pemphigus and fogo selvagem, Brazilian pemphigus, South American pemphigus, wild fire, Brazilian pemphigus (disorder), Amendola's syndrome, Brazilian pemphigus foliaceus, Fogo selvagem, Wildfire pemphigus, Wild fire, Brazilian pemphigus foliaceus (disorder), Brazilian; pemphigus, pemphigus; Brazilian |
| German | Brasilianischer Pemphigus [fogo selvagem] |
| Korean | 브라질 천포창[포고 셀바젬병] |
| Dutch | Braziliaans; pemphigus, pemphigus; Braziliaans, Braziliaanse pemphigus [fogo selvagem] |
| Spanish | fuego salvaje, pénfigo foliáceo brasilero, pénfigo foliáceo brasileño (trastorno), pénfigo foliáceo brasileño, síndrome de Améndola |
