II. Epidemiology
- Rare
- Age of Onset: Under age 5 years
III. Pathophysiology
- Autoimmune bullous disorder
- Variant of Linear IgA Dermatosis (seen in adults)
V. Signs
- Sudden onset of tense inflamed Blisters over red base
- May appear as collarettes of Blisters
- Distribution
- Most commonly found on genitalia
- Also may involves face and perioral skin
- Oral Mucosa involved in 50% of cases
VI. Labs
- Same as Linear IgA Dermatosis
VII. Management
- Same as Linear IgA Dermatosis
VIII. Course
- Resolves within 2 years of onset in most cases