II. Epidemiology

  1. Much less common than Pectus Excavatum
  2. More common in males by ratio of 4:1

III. Causes and associated conditions

IV. Pathophysiology

  1. Softened upper ribs bend forwards
  2. Progresses as child grows

V. Signs

  1. Opposite of Pectus Excavatum
  2. Narrow thorax with increased anteroposterior diameter
  3. Sternum protrudes from chest like keel of ship

VI. Complications

  1. Significant cosmetic concerns

VII. References

  1. Degowin (1987) Bedside Exam, Macmillan, p. 274
  2. Townsend (2001) Sabiston Surgery, p. 1169-70

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Ontology: Congenital pectus carinatum (C0158731)

Definition (MSH) A developmental anomaly characterized by abnormal anterior protrusion of the STERNUM and adjacent COSTAL CARTILAGE.
Concepts Disease or Syndrome (T047) , Congenital Abnormality (T019)
MSH D066166
ICD9 754.82
ICD10 Q67.7
SnomedCT 205101001, 38774000, 157002004, 268348002
English Pectus carinatum, Chicken breast, Congenital pectus carinatum, Pigeon chest, pectus carinatum (diagnosis), pectus carinatum, Keeled breast, Pigeon-chested, Pectus galliatum, Congenital pigeon chest, Congenital pectus carinatum (disorder), Congenital chicken breast, Congenital keeled chest, carinatum pectus, Pectus;carinatum, Carinatum, Pectus, Carinatums, Pectus, Pectus Carinatum, Pectus Carinatums, carinatum; pectus, congenital; pigeon breast or chest, pectus; carinatum, pigeon breast or chest; congenital, Keeled chest, Congenital pigeon breast, pigeon chest
Italian Torace carenato, Petto carenato, Petto a carena, Petto a forma di carena, Pectus carinatum, Con torace carenato
Dutch kippenborst, gekantelde borst, pectus gallinatum, carinatum; pectus, congenitaal; kippenborst, kippenborst; congenitaal, pectus; carinatum, Pectus carinatum, pectus carinatum
French Thorax en carène, Thorax en bréchet, À thorax en carène, Pectus carinatum
German huehnerbruestig, Pectus galliatum, Kielbrust, Huehnerbrust, Pectus carinatum
Portuguese Tórax em quilha, Com peito em carina, Peito em carina, Peito em quilha, Peito quereniforme
Spanish Pectus galliatum, Tórax arqueado, Tórax en quilla, Pecho de pichón, Pecho en quilla, Pecho de paloma, pectus carinatum congénito, pectus carinatum congénito (trastorno), Congenital pectus carinatum, Pectus carinatum
Japanese 鳩胸, 竜骨胸, リュウコツキョウ, キュウキョウ, ハトムネ
Czech Kýlovitý hrudník, Holubí hrudník, Ptačí hrudník, Pectus carinatum, Pectus galliatum
Korean 새가슴
Hungarian Mellkas carinatum, Szegycsont előre állása, Tyúkmell, Előre álló szegycsont, Pectus carinatum, Mellkas galliatum, tyúkmellű