Definition (MSH)
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A group of autosomal-dominant inherited diseases in which COLON CANCER arises in discrete adenomas. Unlike FAMILIAL POLYPOSIS COLI with hundreds of polyps, hereditary nonpolyposis colorectal neoplasms occur much later, in the fourth and fifth decades. HNPCC has been associated with germline mutations in mismatch repair (MMR) genes. It has been subdivided into Lynch syndrome I or site-specific colonic cancer, and LYNCH SYNDROME II which includes extracolonic cancer.
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Concepts |
Neoplastic Process
(T191)
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MSH |
D003123
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English |
Colorectal Neoplasms, Hereditary Nonpolyposis, COLORECTAL NEOPL HEREDITARY NONPOLYPOSIS, HEREDITARY NONPOLYPOSIS COLORECTAL NEOPL, Colorectal Neoplasms, Hereditary Nonpolyposis [Disease/Finding], Familial Nonpolyposis Colon Cancer, Hereditary Nonpolyposis Colorectal Neoplasms |
Swedish |
Icke-polypos kolorektalcancer, ärftlig
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Czech |
kolorektální nádory dědičné nepolypózní
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Finnish |
Periytyvä ei-polypoottinen paksusuolisyöpä
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Russian |
KOLOREKTAL'NYE NOVOOBRAZOVANIIA NASLEDSTVENNYE NEPOLIPOZNYE, NASLEDSTVENNYE NEPOLIPOZNYE KOLOREKTAL'NYE OPUKHOLI, КОЛОРЕКТАЛЬНЫЕ НОВООБРАЗОВАНИЯ НАСЛЕДСТВЕННЫЕ НЕПОЛИПОЗНЫЕ, НАСЛЕДСТВЕННЫЕ НЕПОЛИПОЗНЫЕ КОЛОРЕКТАЛЬНЫЕ ОПУХОЛИ |
Japanese |
リンチ症候群, 遺伝性非ポリポーシス結腸直腸腫瘍, 遺伝性非ポリープ症結腸直腸腫瘍, 遺伝性非ポリポーシス大腸腫瘍, 結腸直腸腫瘍-遺伝性非ポリポーシス, 大腸腫瘍-遺伝性非ポリポーシス, Lynch症候群 |
Polish |
Nowotwory jelita grubego dziedziczne niepolipowe, Nowotwory niepolipowate okrężnicy i odbytnicy dziedziczne, Zespół Lynch, Dziedziczny niepolipowaty rak jelita grubego |
Norwegian |
Arvelige ikke-polyposiske kolorektale svulster, Arvelige ikke-polyposiske kolorektale neoplasmer, Arvelige ikke-polyposiske kolorektale tumorer, Arvelige ikke-polyposiske svulster i tykk- og endetarm, Hereditære ikke-polyposiske kolorektale svulster |
Portuguese |
Neoplasias Colorretais não Polipoides Hereditárias, Câncer Colorretal sem Polipose Hereditário, Câncer Colorretal não Polipoide Hereditário, Neoplasia Colorretal Hereditária sem Polipose, Neoplasias Colorretais Hereditárias sem Polipose, Neoplasias Colorretais sem Polipose Hereditárias |
French |
Tumeurs colo-rectales héréditaires sans polypose, Tumeurs colorectales héréditaires sans polypose, Tumeurs colorectales héréditaires non polyposiques |
German |
Erbliche nichtpolypöse kolorektale Tumoren, Kolorektale Tumoren, hereditäre, ohne Polypose, Kolorektale Tumoren, erbliche, ohne Polypose |
Italian |
Neoplasie del colon e del retto, non poliposi ereditaria
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Dutch |
Carcinomen, Heriditaire non-polyposis-colorectum-, Carcinoom, Heriditair non-polyposis-colorectum-, Colorectumcarcinoom, heriditair non-polyposis-, HNPCC, Heriditair non-polyposis-colorectumcarcinoom, syndroom van Lynch |
Spanish |
Neoplasias Colorrectales Hereditarias sin Poliposis, Neoplasias Colorrectales no Poliposis Hereditarios |