II. History
- Prenatal polyhydramnios in Duodenal Atresia
- Distal Intestine blocked from amniotic fluid absorption
III. Signs
- Duodenal Atresia
- Bilious Emesis
- Absent Abdominal Distention
- Typically presents early, while in newborn nursery
- Distal Small Bowel atresia (jejunum, ileum)
- Symptom onset delayed 12 to 24 hours after first feeding
- Bilious Emesis
- Abdominal Distention
- No meconium passage in first 24 hours in 80% of children
IV. Differential Diagnosis
-
Bilious Emesis and/or delayed meconium passage
- Hirschprung Disease
- Meconium Ileus (Cystic Fibrosis)
- Malrotation with Volvulus
V. Imaging
- Abdominal XRay
- Double Bubble Sign in Duodenal Atresia (large Stomach air filled bubble, smaller duodenal air filled bubble)
- Double-Bubble is also seen in Midgut Volvulus
- Water soluble enemas
- Differentiates atresia from meconium ileus and Hirschprung Disease
- Colon contracted in Intestinal Atresia (obstruction prior to ileocecal valve)
-
Abdominal Ultrasound
- Differentiates atresia from meconium ileus and Intestinal Malrotation
VI. References
- Jones (2022) Crit Dec Emerg Med 36(2): 14-5
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Definition (NCI) | A congenital malformation characterized by the absence of a normal opening in a part of the small intestine. |
Concepts | Congenital Abnormality (T019) |
MSH | C538260 |
SnomedCT | 204694005, 204692009, 84296002 |
English | Atresia of small intest.unsp., Atresia of small intestine, unspecified, Small intestine atresia NOS, atresia of small intestine, atresia of small intestine (diagnosis), Congenital small intestinal atresia, Small intestine atresia, Congenital atresia of the small intestine, Atresia of small intestine, Atresia of the Small Intestine, Small Intestine Atresia, Small intestine atresia NOS (disorder), Atresia of small intestine, unspecified (disorder), Congenital Small Intestine Atresia, Atresia of Small Intestine, Congenital atresia of small intestine, Congenital atresia of small intestine (disorder) |
Italian | Atresia congenita dell'intestino tenue |
Japanese | 先天性小腸閉鎖, センテンセイショウチョウヘイサ |
Spanish | atresia congénita del intestino delgado, atresia del intestino delgado, no especificada (trastorno), atresia del intestino delgado, no especificada, atresia del intestino delgado, SAI, atresia del intestino delgado, SAI (trastorno), Atresia congénita del intestino delgado, atresia congénita del intestino delgado (trastorno), atresia del intestino delgado (trastorno), atresia del intestino delgado |
Czech | Vrozená atrézie tenkého střeva |
Hungarian | Veleszületett vékonybél atresia |
Portuguese | Atresia congénita do intestino delgado |
Dutch | dunne darmatresie, congenitaal |
French | Atrésie congénitale de l'intestin grêle |
German | kongenitale Atresie des Duenndarms |
Ontology: Duodenal atresia (C0266174)
Definition (NCI) | A congenital malformation characterized by the absence of a normal opening in a part of the duodenum. |
Concepts | Congenital Abnormality (T019) |
MSH | C535720 |
SnomedCT | 51118003 |
Italian | Atresia del duodeno, Atresia duodenale congenita |
Dutch | congenitale duodenale atresie, atresie; duodenum, duodenum; atresie, duodenale atresie |
French | Atrésie duodénale congénitale, Atrésie duodénale |
German | Duodenalatresie, kongenital, Duodenalatresie |
Portuguese | Atresia duodenal congénita, Atresia duodenal |
Spanish | Atresia duodenal congénita, atresia congénita de duodeno, atresia duodenal, Atresia duodenal, atresia congénita de duodeno (trastorno), atresia de duodeno (trastorno), atresia de duodeno |
Japanese | 十二指腸閉鎖, 先天性十二指腸閉鎖, センテンセイジュウニシチョウヘイサ, ジュウニシチョウヘイサ |
English | DUODENAL ATRESIA, atresia of duodenum (diagnosis), atresia of duodenum, Duodenal atresia congenital, duodenal atresia, Duodenal atresia, atresia duodenal, Duodenal Atresia, Atresia of Duodenum, Congenital Atresia of Duodenum, Congenital Duodenal Atresia, Congenital atresia of duodenum, Atresia of duodenum, Congenital atresia of duodenum (disorder), atresia; duodenum, duodenum; atresia |
Czech | Atrézie dvanáctníku, Kongenitální atrézie dvanáctníku |
Hungarian | Duodenum atresia, Veleszületett duodenalis atresia |