II. Epidemiology

  1. More common in younger patients
  2. Difficult to diagnose before event occurs

III. Etiology

  1. Anomalous Origin of left Coronary Artery
    1. Associated with acute angle from right sinus
  2. Kawasaki's Disease
    1. Results in Coronary Artery aneurysm

IV. Symptoms

  1. Angina
  2. Palpitations
  3. Syncope with exertion
  4. May present with sudden death
    1. See also Sudden Death in Athletes
    2. Similar to Hypertrophic Cardiomyopathy

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Related Studies

Ontology: Congenital anomaly of coronary artery (C0158623)

Concepts Congenital Abnormality (T019)
ICD9 746.85
SnomedCT 204380003, 204373000, 361215006, 28574005
English Coronary artery anomaly, congenital, Coronary artery abnormality, Coronary artery anomaly NOS, congenital anomaly of coronary artery (diagnosis), congenital anomaly of coronary artery, Congenital coronary artery malformation NOS, anomalies artery coronary, coronary artery anomaly, abnormalities artery coronary, anomaly coronary artery, Coronary artery abnormality (disorder), Coronary artery anomaly NOS (disorder), Coronary arteries--Abnormalities, Congenital coronary artery malformation, Coronary artery anomaly, Congenital anomaly of coronary artery (disorder), Congenital anomaly of coronary artery, coronary artery; anomaly, coronary; artery, anomaly, deformity; artery, coronary, congenital, a.coronaria; anomaly, anomaly; coronary artery, artery; deformity, coronary, congenital, Congenital anomaly of coronary artery, NOS, Coronary artery abnormality [Ambiguous]
Italian Malformazione congenita dell'arteria coronaria, Malformazione congenita di arteria coronaria , NAS, Anomalie dell'arteria coronaria, congenite
Dutch kransslagadermisvorming NAO, congenitaal, congenitale kransslagaderanomalie, a.coronaria; anomalie, anomalie; arteria coronaria, arterie; misvorming, coronair, congenitaal, coronair; arterie, anomalie, coronairarterie; anomalie, misvorming; arterie, coronair, congenitaal, kransslagadermisvorming congenitaal
French Anomalie de l'artère coronaire, congénitale, Malformation congénitale de l'artère coronaire SAI, Malformation congénitale de l'artère coronaire
German kongenitale Anomalie von Koronararterien NNB, Koronararterienanomalie, kongenital, Missbildung der Koronararterien
Portuguese Anomalia congénita das artérias coronárias, Malformação congénita das artérias coronárias NE, Malformação congénita das artérias coronárias
Spanish Malformación congénita de las arterias coronarias NEOM, Anomalía congénita de la arteria coronaria, anomalía de arteria coronaria (trastorno), anomalía de la arteria coronaria, SAI (trastorno), anomalía de la arteria coronaria, SAI, anomalía de arteria coronaria, anomalía congénita de la arteria coronaria (trastorno), anomalía congénita de la arteria coronaria, Malformación congénita de las arterias coronarias
Japanese 先天性冠動脈奇形NOS, 先天性冠動脈奇形, 先天性冠動脈異常, センテンセイカンドウミャクキケイNOS, センテンセイカンドウミャクキケイ, センテンセイカンドウミャクイジョウ
Czech Vrozená anomálie koronární arterie, Vrozená malformace koronární arterie, Vrozená malformace koronární arterie NOS
Hungarian Veleszületett arteria coronaria malformatio k.m.n., Coronaria arteria anomalia, veleszületett, Veleszületett arteria coronaria malformatio

Ontology: Abnormal coronary artery course (C0345122)

Concepts Congenital Abnormality (T019)
SnomedCT 253714001
English Abnorm coronary artery course, Abnormal coronary artery course, Abnormal coronary artery course (disorder)
Spanish trayecto anormal de arteria coronaria (trastorno), trayecto anormal de arteria coronaria