Chiari II Malformation

Aka: Chiari II Malformation, Arnold-Chiari Malformation, Arnold Chiari II Malformation

advertisement

II. Definition: Chiari II Malformation

  1. Cerebellum and Brain Stem elongate via foramen magnum
  2. Cerebellar Tonsils dip into foramen magnum
    1. Risk of cord injury with even minor Trauma

III. Presentation

  1. Presentation as infant (10% of cases)
    1. Apnea
    2. Weak cry
    3. Stridor
      1. Emergency - may herald Respiratory Failure
  2. Insidious course during childhood
    1. Gait Abnormality
    2. Spasticity
    3. Incoordination

IV. Associated Conditions

  1. Myelomeningocele
  2. Hydrocephalus
  3. Corpus callosum abnormalities

V. Management

  1. Management of Myelomeningocele and Hydrocephalus
  2. Decompression of at foramen magnum may be indicated

VI. Precautions

  1. Acute conditions indicating emergent MRI
    1. Head or neck Trauma (even minor Trauma)
    2. Stridor (may herald Respiratory Failure)

VII. References

  1. Majoewsky (2012) EM:Rap-C3 2(9): 5
  2. Behrman (2000) Nelson Pediatrics, Saunders, p. 1810
  3. Goldman (2000) Cecil Medicine, Saunders, p. 2076

Images: Related links to external sites (from Bing)

These images are a random sampling from a Bing search on the term "Chiari II Malformation." Click on the image (or right click) to open the source website in a new browser window. Search Bing for all related images

Related Studies

Related Topics in Cerebellar Disorders

advertisement