Pulmonary Langerhans Cell Granulomatosis

Aka: Pulmonary Langerhans Cell Granulomatosis, Eosinophilic Granuloma, Pulmonary Histiocytosis X, Unifocal Langerhans Cell Histiocytosis

advertisement

II. Pathophysiology

  1. Dendritic Cell disorder

III. Associated Conditions

  1. Letterer-Siwe
  2. Hand-Schuller-Christian Syndrome
  3. Histiocytosis X with Bone involvement

IV. Epidemiology

  1. Ages 20-40 years old
  2. Prior Tobacco use (90%)

V. Signs

  1. See Interstitial Lung Disease

VI. Complications

  1. Pneumothorax (10-30%)
  2. Diabetes Insipidus
  3. Lytic bone lesions (5-10%)

VII. Management

  1. None available

VIII. Coarse

  1. Unpredictable prognosis
  2. Mortality 2-6%

Images: Related links to external sites (from Bing)

These images are a random sampling from a Bing search on the term "Pulmonary Langerhans Cell Granulomatosis." Click on the image (or right click) to open the source website in a new browser window. Search Bing for all related images

Related Studies

Related Topics in Interstitial Lung Disease

advertisement