II. Epidemiology
- Prevalence: 5% of newborns
III. Pathophysiology
- Multiple nipples form in mammalian development
- Mammary glands form along bilateral mammary ridges on the ventral trunk wall
- These ridges course from mid-axilla to inguinal area
- These nipples usually recede in the human Embryo
IV. Signs
- Unilateral or bilateral extra areola and/or nipple
V. Differential diagnosis
- Congenital Melanocytic Nevi (when supernumerary areola present)
VI. Management
- Benign finding that does not require further evaluation or removal
- Previously thought to be associated with renal anomalies, but not supported in recent literature
VII. References
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Related Studies
Concepts | Congenital Abnormality (T019) |
ICD10 | Q83.1 |
SnomedCT | 205604005, 205595005, 18166000, 127857003 |
Italian | Mammella accessoria |
Japanese | 副乳房, フクニュウボウ |
English | POLYMASTIA, POLYTHELIA, FAMILIAL, supernumerary breast (diagnosis), accessory breast (diagnosis), supernumerary breast, accessory breast, Mamma accessoria, accessory breasts, ectopic breast, Ectopic breast (finding), Polymastia, Supernumerary breast, Breast in the wrong place, Ectopic breast, Polymazia, Accessory breast (disorder), breast; aberrant, breast; accessory, breast; supernumerary, extra; breast, aberrant; breast, accessory; breast, polymastia, Ectopic breast (body structure), Ectopic breast (morphologic abnormality), Accessory breast |
Spanish | mama ectópica (estructura corporal), mama ectópica, polimastia, seno accesorio (trastorno), seno accesorio, seno supernumerario, Mama accesoria, mama ectópica (anomalía morfológica) |
German | Akzessorische Mamma, Akzessorische Brust |
Czech | Přídatný prs |
Korean | 부유방 |
Hungarian | Járulékos emlő |
Dutch | aberrant; mamma, accessoir; mamma, extra; mamma, mamma; aberrant, mamma; accessoir, mamma; extra, Accessoire mamma, accessoire borst |
Portuguese | Mama acessória |
French | Mamelle accessoire |
Ontology: Accessory nipple (C0266011)
Concepts | Congenital Abnormality (T019) |
MSH | C562557 |
ICD10 | Q83.3 |
SnomedCT | 157016009, 205605006, 50956007 |
Italian | Capezzolo soprannumerario |
French | Polythélie, Mamelon surnuméraire |
Japanese | 多乳頭, 多乳頭症, タニュウトウ, タニュウトウショウ |
English | Accessory nipples, ACCESSORY NIPPLES, Supernumerary nipples, NIPPLES, SUPERNUMERARY, Accessory nipple, accessory nipple, supernumerary nipple, supernumerary nipple (diagnosis), accessory nipple (diagnosis), breast appearance nipple polythelia, Nipple supernumerary, polythelia, polythelia (physical finding), nipple accessory, extra nipple, hyperthelia, nipple extra, nipples supernumerary, accessory nipples, extra nipples, Supernumerary nipples (polythelia), Accessory Nipples, Polythelia, Familial, Polymastia, Nipples, Supernumerary, Hyperthelia, Polythelia, Supernumerary nipple, Ectopic nipple, Extra nipple, Accessory nipple (disorder), extra; nipple, accessory; nipple, nipple; accessory, nipple; supernumerary, Nipples;supernumerary |
German | Akzessorische Brustwarze, akzessorische Brustwarze |
Czech | Nadpočetná bradavka |
Korean | 부유두 |
Hungarian | Szám feletti mamilla, Mamilla szám feletti |
Dutch | accessoir; tepel, extra; tepel, tepel; accessoir, tepel; extra, Accessoire tepel, overtollige tepel |
Spanish | hipertelia, pezón accesorio (trastorno), pezón accesorio, pezón supernumerario, politelia, Pezón supernumerario |
Portuguese | Mamilo supranumerário |