II. Definitions
- Lymphangioma
- Benign tumor developing as a Congenital Abnormality of the lymph system
- Results in dilated lymph channels
III. Epidemiology
- Onset under age 2 years (typically as a young infant)
IV. Pathophysiology
V. Associated Conditions
- Turner's Syndrome
- Noonan's Syndrome
- Down Syndrome
VI. Symptoms
- Initial
- Asymptomatic
- Painless lesion unless infected or bleeding
- Progression: Continues to increases in size
- 90% symptomatic by age 2 years
VII. Signs
- Fluctuant mass usually in neck
- Mass transilluminates
VIII. Complications
- Infection
- Bleeding
- Airway compromise (due to compression)
IX. Differential Diagnosis
X. Imaging
-
Chest XRay
- Identify mediastinal extension
- Pleural Effusion
XI. Management
- Deliver where NICU available if diagnosed prenatally
- Risk of airway compromise
- Surgical excision
XII. Prognosis
- Recurrence rate after surgical excision: 10-15%
XIII. References
- Townsend (2001) Sabiston Surgery, Saunders, p. 546-7
- Muensterer (2000) Pediatr Rev 21(4):139-43 [PubMed]
- Weintraub (2000) Otolaryngol Clin North Am 33:1171-89 [PubMed]
Images: Related links to external sites (from Bing)
Related Studies
| Definition (MSH) | A benign tumor resulting from a congenital malformation of the lymphatic system. Lymphangioendothelioma is a type of lymphangioma in which endothelial cells are the dominant component. |
| Definition (NCI_CDISC) | A benign neoplasm arising from the lymphatics. |
| Definition (NCI) | A benign neoplasm arising from the lymphatics. The tumor is composed of dilated lymphatic channels. Painless swelling is the usual clinical manifestation. |
| Concepts | Neoplastic Process (T191) |
| MSH | D008202 |
| ICD9 | 228.1 |
| ICD10 | D18.1 , M9170/0 |
| SnomedCT | 69044001, 189200000, 154625006, 189875000, 93168006, 269646001, 400178008, 254836000, 253057002 |
| English | Lymphangioma, Lymphangiomas, Lymphangioma, any site, LYMPHANGIOMA, Lymphangioma NOS, [M]Lymphangioma NOS, benign lymphangioma, benign lymphangioma (diagnosis), Lymphangioma, no ICD-O subtype, Lymphangioma [Disease/Finding], lymphangiomas, congenital lymphangioma, lymphangioma, [M]Lymphangioma NOS (morphologic abnormality), Lymphangioma of unspecified site (disorder), Lymphangioma of unspecified site, Lymphangioma, no International Classification of Diseases for Oncology subtype (morphologic abnormality), Lymphangioma, no International Classification of Diseases for Oncology subtype, Lymphangioma, no ICD-O subtype (morphologic abnormality), LYMPHANGIOMA, BENIGN, Congenital lymphangioma, Lymphangioma morphology, Benign lymphangioma, Congenital lymphangioma (disorder), Lymphangioma (disorder), Lymphangioma, site unspecified, Benign lymphangioma (morphologic abnormality), Lymphangioma, NOS |
| French | LYMPHANGIOME, Lymphangiome, site non précisé, Lymphangiome |
| Portuguese | LINFANGIOMA, Linfangioma de qualquer localização, Linfangioma |
| Spanish | LINFANGIOMA, morfología: linfangioma, no clasificado como subtipo en CIE - O, Linfangioma de cualquier localización, [M]linfangioma, SAI, linfangioma de localización no especificada (trastorno), [M]linfangioma, SAI (anomalía morfológica), linfangioma (trastorno), linfangioma benigno (anomalía morfológica), linfangioma benigno, linfangioma congénito (trastorno), linfangioma congénito, linfangioma de localización no especificada, linfangioma, SAI, linfangioma, morfología de linfangioma, morfología: linfangioma, no clasificado como subtipo en CIE - O (anomalía morfológica), Linfangioma |
| German | LYMPHANGIOM, Lymphangiom, beliebige Stelle, Lymphangiom, jede Lokalisation, Lymphangiom |
| Dutch | lymfangioom, elke plaats, Lymfangioom, elke lokalisatie, lymfangioom, Angioom, lymf-, Lymfangioom |
| Italian | Linfangioma, ogni sede, Linfangioma |
| Japanese | リンパ管腫、部位を限定しない, ﾘﾝﾊﾟｶﾝｼｭ, ﾘﾝﾊﾟｶﾝｼｭﾌﾞｲｦｹﾞﾝﾃｲｼﾅｲ, リンパ管腫-海綿状, リンパ管内皮腫, リンパ管腫, 海綿状リンパ管腫 |
| Swedish | Lymfangiom |
| Czech | lymfangiom, Lymfangiom, Lymfangiom kterékoliv lokalizace |
| Finnish | Lymfangiooma |
| Russian | LIMFANGIOMA, LIMFANGIOENDOTELIOMA, ЛИМФАНГИОМА, ЛИМФАНГИОЭНДОТЕЛИОМА |
| Korean | 모든 부위의 림프관종 |
| Polish | Śródbłoniak limfatyczny, Naczyniak limfatyczny |
| Hungarian | Lymphangioma, bármely hely, Lymphangioma |
| Norwegian | Lymfangiom |
Ontology: Cavernous lymphangioma (C0205828)
| Definition (NCI) | A lymphangioma characterized by the presence of thin-walled cavernous lymphatic spaces. |
| Concepts | Neoplastic Process (T191) |
| MSH | D008202 |
| ICD10 | M9172/0 |
| SnomedCT | 89056007 |
| English | Cavernous Lymphangiomas, Lymphangiomas, Cavernous, Cavernous Lymphangioma, Cavernous lymphangioma, Cavernous lymphangioma (morphologic abnormality), cavernous; lymphangioma, lymphangioma; cavernous, Lymphangioma, Cavernous |
| Portuguese | Linfangioma Cavernoso |
| Spanish | Linfangioma Cavernoso, linfangioma cavernoso (anomalía morfológica), linfangioma cavernoso |
| French | Lymphangiome caverneux |
| German | Lymphangiom, kavernöses |
| Italian | Linfangioma cavernoso |
| Norwegian | Kavernøst lymfangiom |
| Dutch | caverneus; lymfangioom, lymfangioom; caverneus, Lymfangioom, caverneus |
Ontology: Lymphangioma, Cystic (C0206620)
| Definition (NCI) | A benign lymphatic neoplasm usually arising from the neck and characterized by cystic dilation of the lymphatic vessels. |
| Definition (MSH) | A cystic growth originating from lymphatic tissue. It is usually found in the neck, axilla, or groin. |
| Concepts | Neoplastic Process (T191) |
| MSH | D018191 |
| ICD10 | M9173/0 |
| SnomedCT | 423984004, 40225001, 399882002 |
| English | Hygroma cystic, Hygroma, Hygroma, Cystic, Lymphangioma, Cystic, Cystic Hygromas, Cystic Lymphangiomas, Hygromas, Hygromas, Cystic, Lymphangiomas, Cystic, Cystic Hygroma, Cystic Lymphangioma, Non-neoplastic hygroma (disorder), Non-neoplastic hygroma, HYGROMA CYSTIC, Colli, Cystic Hygroma, Hygroma Colli, Cystic, Cystic Hygroma Colli, Lymphangioma, Cystic [Disease/Finding], cystic hygroma, cystic lymphangioma, cystic lymphangiomas, hygromas, cystic hygromas, Cystic lymphangioma, Cystic hygroma, Cystic hygroma (disorder), Cystic lymphangioma (morphologic abnormality), cystic; lymphangioma, hygroma, lymphangioma; cystic, Hygroma, NOS, Lymphangioma;cystic |
| Dutch | cystisch hygroom, hygroom cystisch, cysteus; lymfangioom, lymfangioom; cysteus, cystisch lymfangioom, Cystisch lymfangioom, Hygroom, Hygroom, cystisch, Lymfangioom, cystisch |
| German | zystisches Hygrom, Hygrom, zystisch, HYGROMA CYSTICUM, zystisches Lymphangiom, Hygrom, zystisches, Hygrom, Lymphangiom, zystisches |
| Portuguese | Higroma quístico, HIGROMA QUISTICO, Linfangioma cístico, Higroma Cístico, Higroma, Linfangioma Cístico |
| Spanish | Higroma quístico, higroma no neoplásico, higroma no neoplásico (trastorno), higroma quístico (trastorno), higroma quístico, higroma, linfangioma quístico (anomalía morfológica), linfangioma quístico, Linfangioma cístico, Higroma Quístico, Higroma, Linfangioma Quístico |
| Japanese | 水滑性嚢腫, ﾉｳﾎｳｾｲﾘﾝﾊﾟｶﾝｼｭ, ﾉｳﾎｳｾｲﾋｸﾞﾛｰﾏ, ｽｲｶﾂｾｲﾉｳｼｭ, リンパ管腫-嚢胞性, 嚢腫性リンパ管腫, のう胞性リンパ管腫, ヒグローマ, 嚢胞性ヒグローマ, 嚢胞性リンパ管腫, ヒグローマ-嚢胞性 |
| Swedish | Lymfangiom, cystiskt |
| Czech | lymfangiom cystický, Cystický lymfangiom, Hygroma cysticum, Cystický hygrom |
| Finnish | Imusuonirakko |
| Russian | GIGROMA, LIMFANGIOMA KISTOZNAIA, GIGROMA KISTOZNAIA, ГИГРОМА, ГИГРОМА КИСТОЗНАЯ, ЛИМФАНГИОМА КИСТОЗНАЯ |
| French | HYGROMA KYSTIQUE, Hygrome kystique, Lymphangiome kystique, Hygroma kystique |
| Italian | Igroma cistico, Igroma, Linfangioma cistico |
| Polish | Wodniak torbielowaty, Hygroma, Naczyniak limfatyczny torbielowaty |
| Hungarian | Hygroma cystikus, Cystikus lymphangioma, Cystikus hygroma |
| Norwegian | Cystisk hygrom, Cystisk lymfangiom |
