II. Epidemiology
- Rare pregnancy-related disorder
III. Pathophysiology
- Generalized Pustular Psoriasis variant specific to pregnancy
IV. Symptoms
- Rash develops in third trimester
- No Pruritus
- Contrast with nearly every other specific cause of Skin Conditions of Pregnancy
- See Pruritus in Pregnancy
- Systemic symptoms may develop (related to complications)
V. Signs: Skin
-
Pustular Psoriasis
- Starts as Pustules
- Pustular lesions coalesce into Plaques
- Plaques desquamate
- Lesion Distribution
- Starts in the intertriginous areas (e.g. inguinal and axillary folds)
- Spreads centrifugally to the extremities
- Spares the face, palms and soles
- Associated Findings
VI. Management
- Increased antepartum observation (fetal surveillance)
- High dose Systemic Corticosteroids
- Prednisone 20-60 mg daily with taper
- Severe cases
-
Antibiotics
- As indicated for secondary Skin Infections
VII. Complications: Maternal
- Secondary Bacterial Infection (may be systemic)
- Hyperparathyroidism
- Hypocalcemia
- Hypoalbuminemia
VIII. Complications: Fetus
- Adverse fetal outcomes
- Placental insufficiency
- Fetal demise
IX. Course
- Onset in third trimester of pregnancy
- Resolves after delivery
- May recur with future pregnancies
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Related Studies
Concepts | Disease or Syndrome (T047) |
SnomedCT | 238613007 |
English | Gen pust psoriasis of pregnanc, Generalised pustular psoriasis of pregnancy, Generalized pustular psoriasis of pregnancy, Generalized pustular psoriasis of pregnancy (disorder) |
Spanish | psoriasis pustulosa generalizada del embarazo (trastorno), psoriasis pustulosa generalizada del embarazo |
Ontology: Impetigo herpetiformis (C1314968)
Concepts | Disease or Syndrome (T047) |
ICD9 | 694.3 |
ICD10 | L40.1 |
SnomedCT | 65539006, 200973000 |
Italian | Impetigine erpetiforme |
Japanese | 疱疹状膿痂疹, ホウシンジョウノウカシン |
English | impetigo herpetiformis, impetigo herpetiformis (diagnosis), Impetigo herpetiformis (disorder), herpetiformis; impetigo, impetigo; herpetiformis, Impetigo herpetiformis |
Czech | Impetigo herpetiformis |
Hungarian | Impetigo herpetiformis |
Dutch | herpetiformis; impetigo, impetigo; herpetiformis, impetigo herpetiformis |
Spanish | impétigo herpetiforme (trastorno), impétigo herpetiforme, Impétigo herpetiforme |
Portuguese | Impetigo herpetiforme |
French | Impétigo herpétiforme |
German | Impetigo herpetiformis |