Definition (MSHCZE)
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Onemocnění ledvin vyskytující se obv. u dětí, charakterizované nefrotickým syndromem s velkými ztrátami bílkovin močí. Podstatou jsou změny glomerulu (glomerulopatie), které jsou patrny jen elektronovým mikroskopem (nověji se užívá termínu „minimal changes disease"). V léčbě jsou účinné kortikoidy. (cit. Velký lékařský slovník online, 2012 http://lekarske.slovniky.cz/ )
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Definition (MSH)
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A kidney disease with no or minimal histological glomerular changes on light microscopy and with no immune deposits. It is characterized by lipid accumulation in the epithelial cells of KIDNEY TUBULES and in the URINE. Patients usually show NEPHROTIC SYNDROME indicating the presence of PROTEINURIA with accompanying EDEMA.
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Concepts |
Disease or Syndrome
(T047)
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MSH |
D009402
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ICD10 |
N04
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SnomedCT |
197592009, 44785005 |
English |
Minimal change nephrotic syndrome, Lipoid Nephroses, Lipoid Nephrosis, Minimal Change Nephropathies, Nephropathies, Minimal Change, Nephropathy, Minimal Change, Nephroses, Lipoid, Nephrosis, Lipoid, Minimal Change Nephropathy, Idiopathic nephrotic syndrome, Light negative GN, MCN - Minimal change nephrop, Minimal change nephrotic synd, Glomerulopathies, Minimal Change, Glomerulopathy, Minimal Change, Minimal Change Glomerulopathy, lipoid nephrosis, Nephrosis, Lipoid [Disease/Finding], change diseases minimal, nephrosis lipoid, change glomerulonephritis minimal, change disease minimal, changes glomerulonephritis minimal, minimal change nephropathy, nil disease, minimal change disease, disease nils, Diseases, Minimal Change, Minimal Change Disease, Idiopathic Minimal Change Nephrotic Syndrome, Disease, Minimal Change, Minimal Change Diseases, Change Diseases, Minimal, Minimal change nephropathy, Lipid nephrosis, Minimal change disease, Nil disease, Light negative glomerulonephritis, MCD - Minimal change disease, MCN - Minimal change nephropathy, Minimal change disease (disorder), lipoid; nephrosis, nephrosis; lipoid, Lipoid nephrosis, Foot process disease |
Dutch |
minimale verandering in ziekte, lipoïdenefrose, lipoïd; nefrose, nefrose; lipoïd, Glomerulopathy, minimal-change, Nefrotisch syndroom, 'minimal-change', Nephropathy, minimal-change, Lipoïde nefrose, Nefrose, lipoïde |
French |
Maladie à changement minime, Néphrose lipoïdique, Néphropathie à lésion glomérulaire minime, Syndrome néphrotique pur, Syndrome néphrotique à lésions glomérulaires minimes |
German |
Minimal-changes-GP, Minimal Change Glomerulopathie, Minimal Change Nephrose, Lipoid-Nephrose, Minimal-Change-Glomerulopathie, Minimal-Change-Nephrose, Nephrose, Lipoid-, Lipoidnephrose |
Italian |
Malattia a lesioni minime, Nefrosi lipoidea, Nefrosi lipoide |
Portuguese |
Doença de alteração mínima, Nefrose lipóide, Glomerulopatia de Lesões Mínimas, Nefrose Lipoide, Nefropatia de Lesões Mínimas |
Spanish |
Nefrosis lipoide, Enfermedad de cambios mínimos, Nefropatía de Cambios Mínimos, Glomerulopatía de Cambios Mínimos, Síndrome Nefrótico de Lesión Mínima, Síndrome Nefrótico de Variación Mínima, Glomerulonefritis de Lesiones Mínimas, Glomerulopatía de Lesiones Mínimas, Síndrome Nefrótico de Lesiones Mínimas, enfermedad de Nil, enfermedad de cambios mínimos, glomerulopatía con cambios mínimos (trastorno), glomerulopatía con cambios mínimos, nefrosis lipoidea, Nefrosis Lipoidea |
Japanese |
微小変化群, リポイドネフローゼ, ビショウヘンカグン, 糸球体腎炎-微少変化, ネフローゼ-リポイド, リポイドネフローゼ, リポイド変性ネフローゼ, 微小変化ネフローゼ症候群, 微小変化糸球体腎炎, 微小変化腎症, 類脂質変性ネフローゼ, ネフローゼ-リポイド変性, ネフローゼ-類脂質変性, ネフローゼ症候群-微小変化型, ネフローゼ症候群-微少変化, 微小変化型ネフローゼ症候群, 微少変化ネフローゼ症候群, 微少変化型ネフローゼ症候群, 微少変化型糸球体腎炎, 微少変化型腎症, 微少変化糸球体腎炎, 微少変化腎症, 腎症-微少変化, 類脂ネフローゼ, 類脂変性ネフローゼ, 類脂質ネフローゼ |
Swedish |
Lipoidnefros
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Finnish |
Lipoidinefroosi
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Russian |
NEFROPATIIA, MINIMAL'NYE IZMENENIIA, NEFROZ LIPOIDNYI, GLOMERULONEFRIT, MINIMAL'NYE IZMENENIIA, NEFROTICHESKII SINDROM, MINIMAL'NYE IZMENENIIA, ГЛОМЕРУЛОНЕФРИТ, МИНИМАЛЬНЫЕ ИЗМЕНЕНИЯ, НЕФРОЗ ЛИПОИДНЫЙ, НЕФРОПАТИЯ, МИНИМАЛЬНЫЕ ИЗМЕНЕНИЯ, НЕФРОТИЧЕСКИЙ СИНДРОМ, МИНИМАЛЬНЫЕ ИЗМЕНЕНИЯ |
Czech |
Lipoidní nefróza, Glomerulonefritida s minimálními změnami, nefróza lipoidní, nemoc minimálních změn, glomerulopatie s minimálními změnami, idiopatický nefrotický syndrom s minimálními změnami, lipoidní nefróza |
Polish |
Nerczyca lipidowa
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Hungarian |
Lipoid nephrosis, Minimal-change betegség |
Croatian |
NEFROZA, LIPOIDNA
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Norwegian |
Lipoid nefrose
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