II. Epidemiology
- Uncommon congenital Cardiomyopathy (<1% of population)
III. Pathophysiology
- Disordered in-utero development of mature heart Muscle
- Increased trabeculation of Myocardium
- Development of increased intertrabecular recesses within the left ventricle
- Results in Left Ventricular Dysfunction
- Heart Failure
- Arrhythmia
- Thromboembolic disease
- Sudden Cardiac Death
IV. Findings
V. Diagnosis
-
Echocardiogram
- Initial, first-line test
-
Cardiac MRI
- Confirms diagnosis
VI. Management
- See Congestive Heart Failure
-
Anticoagulation indications
- Atrial Fibrillation
- Decreased systolic function
- Systemic Thromboembolism or intracardiac thrombus