II. Definitions

  1. Dermatofibrosarcoma Protuberans
    1. Low grade fibroblastic tumor presents as a firm, nodular, Subcutaneous Mass of the trunk or proximal extremities
    2. Locally destructive but rarely metastasizes

III. Epidemiology

  1. Onset ages 20 to 59 years old
  2. No gender predominance
  3. Rare (accounts for 1% of Soft Tissue Sarcomas)

IV. Findings

  1. Slow growing Subcutaneous Nodule with overlying pink Plaque
  2. Advanced lesions may ulcerate and bleed
  3. Distribution
    1. Trunk: 50 to 60%
    2. Proximal arms: 25%
    3. Head and Neck: 10 to 15%

V. Imaging

  1. Ultrasound
    1. Hypervascularity
    2. Tentacle-like projections

VI. Management

  1. Refer to orthopedic oncology for core needle biopsy and wide surgical resection

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