II. Definitions
- Dermatofibrosarcoma Protuberans
- Low grade fibroblastic tumor presents as a firm, nodular, Subcutaneous Mass of the trunk or proximal extremities
- Locally destructive but rarely metastasizes
III. Epidemiology
- Onset ages 20 to 59 years old
- No gender predominance
- Rare (accounts for 1% of Soft Tissue Sarcomas)
IV. Findings
- Slow growing Subcutaneous Nodule with overlying pink Plaque
- Advanced lesions may ulcerate and bleed
- Distribution
- Trunk: 50 to 60%
- Proximal arms: 25%
- Head and Neck: 10 to 15%
V. Imaging
-
Ultrasound
- Hypervascularity
- Tentacle-like projections
VI. Management
- Refer to orthopedic oncology for core needle biopsy and wide surgical resection