Definition (NCI)
|
A syndrome characterized by polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes. It is often associated with osteosclerotic myeloma.
|
Definition (MSH)
|
A multisystemic disorder characterized by a sensorimotor polyneuropathy (POLYNEUROPATHIES), organomegaly, endocrinopathy, monoclonal gammopathy, and pigmentary skin changes. Other clinical features which may be present include EDEMA; CACHEXIA; microangiopathic glomerulopathy; pulmonary hypertension (HYPERTENSION, PULMONARY); cutaneous necrosis; THROMBOCYTOSIS; and POLYCYTHEMIA. This disorder is frequently associated with osteosclerotic myeloma. (From Adams et al., Principles of Neurology, 6th ed, p1335; Rev Med Interne 1997;18(7):553-62)
|
Concepts |
Disease or Syndrome
(T047)
|
MSH |
D016878
|
SnomedCT |
79268002
|
English |
Crow Fukase Syndrome, Crow-Fukase Syndrome, POEMS Syndrome, Syndrome, Crow-Fukase, Syndrome, POEMS, Syndrome, Takatsuki's, Takatsuki Syndrome, Takatsuki's Syndrome, POEMS - Poly org endo mono syn, POEMS - Polyneurpath organomegal endocrinop moncl+skin chan, Polyn orgomeg endoc monoclon s, Polyneuropathy organomegaly endocrinop monoc gam+skin chang, POEMS syndrome (disorder), Polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS) syndrome, POEMS, POEMS syndrome (diagnosis), POEMS Syndrome [Disease/Finding], Polyneuropathy, Organomegaly, Endocrinopathy, M Protein, and Skin Changes Syndrome, Polyneuropathy Organomegalies, Organomegaly, Polyneuropathy, Polyneuropathy Organomegaly, Organomegalies, Polyneuropathy, crow-fukase syndrome, poem syndrome, poems syndrome, Polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS) syndrome (disorder), Polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes syndrome (disorder), Polyneuropathy, organomegaly, endocrinopathy, M-protein, and skin changes, Crow-Fukase syndrome, POEMS syndrome, POEMS - Polyneuropathy organomegaly endocrinopathy monoclonal and skin changes, Polyneuropathy organomegaly endocrinopathy monoclonal gammopathy and skin changes, Polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes syndrome, Polyneuropathy organomegaly endocrinopathy monoclonal gammopathy and skin changes (disorder) |
Japanese |
POEMS症候群, クロウ・深瀬症候群, クロウフカセショウコウグン, POEMSショウコウグン, Crow-深瀬症候群, Crow-Fukase症候群, POEMS症候群, 多発ニューロパチー・臓器肥大・内分泌障害・M蛋白および皮膚病変, タハツニューロパチーゾウキヒダイナイブンピツショウガイMタンパクオヨビヒフビョウヘン, タハツニューロパチーゾウキヒダイナイブンピショウガイMタンパクオヨビヒフビョウヘン, クロウ-深瀬症候群, 高月病, 高月症候群 |
Swedish |
POEMS-syndrom
|
Spanish |
síndrome de polineuropatía, organomegalia, endocrinopatía, gammapatía monoclonal y cambios cutáneos (POEMS), síndrome POEMS (trastorno), síndrome de polineuropatía, organomegalia, endocrinopatía, gammapatía monoclonal y cambios cutáneos (POEMS) (trastorno), síndrome de polineuropatía, organomegalia, endocrinopatía, gammapatía monoclonal y cambios cutáneos (trastorno), Polineuropatía, organomegalia, endocrinopatía, proteína M y cambios cutáneos, síndrome POEMS, síndrome de polineuropatía, organomegalia, endocrinopatía, gammapatía monoclonal y cambios cutáneos, síndrome de polineuropatía, organomegalia, endocrinopatía, gammapatía monoclonal y modificaciones de la piel, Síndrome de Crow-Fukase, Síndrome de Takatsuki, Síndrome POEMS |
Czech |
Crow-Fukase syndrom, syndrom POEMS, Takatsuki syndrom, Crow-Fukasův syndrom, POEMS syndrom, Myelom s nervovými poruchami, organomegalií, endokrinopatií, kožními změnami |
Finnish |
POEMS-oireyhtymä
|
Russian |
TAKATZUKI SINDROM, POEMS SINDROM, POEMS СИНДРОМ, ТАКАТЗУКИ СИНДРОМ |
Italian |
Sindrome di Takatsuki, Sindrome di Crow-Fukase, Polineuropatia, organomegalia, endocrinopatia, proteina M e variazioni cutanee, Sindrome POEMS |
Polish |
Zespół Crow-Fukase, Zespół Takatsuki, Zespół POEMS |
Hungarian |
Crow-Fukase syndroma, POEMS-syndroma, Polyneuropathia, organomegalia, endocrinopathia, M-protein és bőrelváltozások |
Norwegian |
Syndrom med polynevropati, organomegali, endokrinopati, monoklonal gammopati og hudforandringer, POEMS-syndrom |
Dutch |
polyneuropathie, organomegalie, endocrinopathie, M-proteïne en huidafwijkingen, Crow-Fukase-syndroom, POEMS-syndroom, Syndroom, POEMS-, Takatsuki-syndroom |
French |
Polyneuropathie, organomégalie, endocrinopathie, Protéine M et signes cutanés, Syndrome POEMS, Syndrome de Crow-Fukase, Syndrome de Takatsuki |
German |
Polyneuropathie, Organomegalie, Endokrinopathie, M-Protein- und Hautveraenderungen, POEMS Syndrom, Crow-Fukase-Syndrom, POEMS-Syndrom, Takatsuki-Syndrom |
Portuguese |
Polineuropatia, organomegalia, endocrinopatia, proteína M e alterações da pele, Síndrome de POEMS, Síndrome de Crow-Fukase, Síndrome de Takatsuki, Síndrome POEMS |