II. Epidemiology

  1. Endemic regions
    1. Central Europe
    2. Siberia
    3. North America
      1. North central United States and Canada
      2. Alaska (Eskimos)
  2. Definitive Host: Fox
  3. Intermediate host: Rodents. Humans

III. Etiology

  1. Echinococcus multilocularis

IV. Pathophysiology

  1. Caused by larvae of cestode Echinococcus multilocularis
  2. Causes a highly malignant form of Echinococcosis
    1. Primary infection site is liver
    2. Spreads contiguously in cancer like form
    3. Ultimately results in death by hepatic insufficiency
    4. Lung or brain metastases may occur

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Ontology: Echinococcus multilocularis (C0322178)

Definition (MSH) A north temperate species of tapeworm (CESTODA) whose adult form infects FOXES and wild RODENTS. The larval form can infect humans producing HEPATIC HYDATID CYSTS.
Concepts Eukaryote (T204)
MSH D048210
SnomedCT 86648009
English Echinococcus multilocularis, Echinococcus multiloculari, multilocularis, Echinococcus, multiloculari, Echinococcus, Alveolar hydatid, Echinococcus multilocularis (organism)
Swedish Echinococcus multilocularis
Czech Echinococcus multilocularis, měchožil větvený, měchožil bublinatý, tasemnice liščí
Finnish Echinococcus multilocularis
Russian EKHINOKOKK IACHEISTYI, ECHINOCOCCUS MULTILOCULARIS, ЭХИНОКОКК ЯЧЕИСТЫЙ
French Échinocoque du renard, Ténia échinocoque du renard, Echinococcus multilocularis
Polish Echinococcus multilocularis
Norwegian Echinococcus multilocularis, Revens dvergbendelorm
Spanish Echinococcus multilocularis (organismo), hidátide alveolar, Echinococcus multilocularis
German Echinococcus multilocularis
Italian Echinococcus multilocularis
Dutch Echinococcus multilocularis
Portuguese Echinococcus multilocularis