II. Pathophysiology

III. Causes: Congenital Coagulopathy (Severe Hereditary Bleeding Disorders)

V. Signs: Presentations

  1. See Bleeding Disorder
  2. Hemophilia A or B often presents with bleeding complications shortly after birth
    1. Cephalohematoma or Intracranial Hemorrhage
    2. Significant bleeding from Circumcision site
  3. Other common presentations
    1. Gingival Bleeding
    2. Minor Trauma with significant bleeding or large Hematomas
    3. Severe Menorrhagia (common delayed presentation in Von Willebrand's Disease)

Images: Related links to external sites (from Bing)

Related Studies

Ontology: Blood Coagulation Disorders (C0005779)

Definition (MSHCZE) Nemoc charakterizovaná zvýšenou krvácivostí způsobenou nedostatkem nebo poruchou koagulačních faktorů, popř. přítomností jejich inhibitorů. Může být dědičná hemofilie nebo získaná např. při těžkých jaterních chorobách, poruše vstřebávání vitaminu K. (cit. Velký lékařský slovník online, 2012 http://lekarske.slovniky.cz/ )
Definition (SCTSPA) Trastornos que afectan a los elementos de la coagulación sanguínea, incluidos plaquetas, factores e inhibidores de la coagulación y el sistema fibrinolítico
Definition (SNOMEDCT_US) Disorders involving the elements of blood coagulation, including platelets, coagulation factors and inhibitors, and the fibrinolytic system
Definition (NCI) A condition in which there is a deviation from or interruption of the normal coagulation properties of the blood.
Definition (MSH) Hemorrhagic and thrombotic disorders that occur as a consequence of abnormalities in blood coagulation due to a variety of factors such as COAGULATION PROTEIN DISORDERS; BLOOD PLATELET DISORDERS; BLOOD PROTEIN DISORDERS or nutritional conditions.
Definition (CSP) condition in which there is a deviation from or interruption of the normal coagulation properties of the blood.
Concepts Disease or Syndrome (T047)
MSH D001778
ICD9 286
ICD10 D68.9
SnomedCT 64779008, 267562007, 154815003, 127073005, 191303002, 362970003
English Blood Coagulation Disorder, Blood Coagulation Disorders, Coagulation Disorder, Blood, Coagulation Disorders, Blood, Disorder, Blood Coagulation, Disorders, Blood Coagulation, COAGULATION DISORDER, blood coagulation disorder, Coagulation defect NOS, Coagulation defect, unspecified, BLOOD COAG DIS, COAG DIS BLOOD, DIS BLOOD COAG, clotting disorder, coagulation defects (diagnosis), coagulation defects, Coagulation abnormal, Defect coagulation (NOS), Coagulation disorder (NOS), Coagulation disorder NOS, Disorder coagulation, Blood coagulation disorder, NOS, Disorder of haemostasis, NOS, Coagulopathy, NOS, Coagulation disorder, NOS, Blood clotting disorder, NOS, Disorder of hemostasis, NOS, Blood Coagulation Disorders [Disease/Finding], coagulation disorder, Abnormal;coagulation, bleeding diathesis, coagulation disorders, coagulopathies, blood coagulation disorders, bleeding tendency, bleeding disorders, blood clotting disorder, hemostatic disorder, bleeding disorder, blood clotting disorders, clotting disorders, disorders of coagulation, Coagulopathies, Coagulation defects, Clotting disorders, (Coagulation defects) or (bleeding disorders), (Coagulation defects) or (bleeding disorders) (disorder), Coagulation defect NOS (disorder), Disorder of hemostasis (disorder), Blood coagulation disorders, Coagulation Defect, COAGULOPATHY, Coagulopathy, Disorder of hemostasis, Clotting disorder, Coagulation disorder, Disorder of haemostasis, Disorder of haemostatic system, Disorder of hemostatic system (disorder), Disorder of hemostatic system, Blood clotting disorder, Blood coagulation disorder (disorder), Blood coagulation disorder, coagulopathy, blood clotting; disorder, coagulation defect, disorder; blood clotting, disorder; hemostasis, disturbance; blood clotting, Coagulation Disorder, Disorder, coagulation, Disorder, hemostasis, Defective coagulation NOS, abnormal coagulation
Italian Coagulopatia, Coagulopatie, Deficit della coagulazione (NAS), Disturbo della coagulazione, Disturbo della coagulazione (NAS), Coagulazione anormale, Disturbo della coagulazione, NAS, Difetti della coagulazione, Patologia della coagulazione, Difetti della coagulazione del sangue
Dutch coagulatiestoornis NAO, stollingsstoornis, stollingsafwijking, stolling abnormaal, stollingsstoornis (NAO), coagulatieaandoening, coagulatieaandoening NAO, stollingsstoornissen, bloedstolling; stoornis, stoornis; bloedstolling, stoornis; hemostase, Stollingsstoornis, niet gespecificeerd, coagulopathie, coagulopathieën, Bloedstollingsstoornis, Coagulopathie
French Trouble de la coagulation, Coagulation anormale, Trouble de la coagulation SAI, Anomalies de coagulation, Défaut de coagulation SAI, TROUBLE DE LA COAGULATION, Coagulopathie, Coagulopathies, Troubles de l'hémostase et de la coagulation, Troubles de la coagulation sanguine
German Blutgerinnungsstoerung, Blutgerinnungsstoerung (NNB), Blutgerinnungsstoerung NNB, Stoerung, Blutgerinnung, Defekt, Blutgerinnung (NNB), Blutgerinnung anomal, Gerinnungsstoerung, Blutgerinnungsdefekte, KOAGULATIONSSTOERUNG, Koagulopathie, nicht naeher bezeichnet, Koagulopathie, Koagulopathien, Blutgerinnungsstörungen, Gerinnungsstörungen
Portuguese Defeitos da coagulação, Perturbação da cogulação, Afecção da coagulação, Defeito de coagulação NE, Perturbação da coagulação, Perturbação da coagulação NE, Coagulação anormal, ALTERACAO DA COAGULACAO, Coagulopatia, Coagulopatias, Transtornos da Coagulação Sanguínea
Spanish Trastorno de la coagulación NEOM, Coagulación anormal, Defecto de la coagulación (NEOM), Trastorno de la coagulación (NEOM), Defectos de coagulación, Trastorno de la coagulación, Alteración de coagulación, COAGULACION, TRASTORNO, Trastornos de la Coagulación Sanguínea, defecto de la coagulación, SAI (trastorno), trastorno de la hemostasia (concepto no activo), trastorno de la hemostasia, defecto de la coagulación, SAI, coagulopatía, defecto de la coagulación, trastorno de la coagulación sanguínea (trastorno), trastorno de la coagulación sanguínea, trastorno del sistema hemostático (trastorno), trastorno del sistema hemostático, Coagulopatías, Coagulopatía
Japanese 凝固異常, 凝固欠損(NOS), 凝固不全, 凝固障害NOS, 凝血異常, 凝固障害(NOS), 凝固障害, ギョウコショウガイNOS, ギョウコケッソンNOS, ギョウコイジョウ, ギョウコフゼン, ギョウコショウガイ, ギョウケツイジョウ, 血液凝固異常, 血液凝固障害
Swedish Blodkoagulationsstörningar
Czech koagulopatie, krev - poruchy koagulace, Abnormální koagulace, Poruchy krevního srážení, Koagulopatie (NOS), Porucha srážení krve, Poruchy krevní srážlivosti, Koagulopatie, Porucha krevního srážení NOS, Porucha krevního srážení (NOS), koagulační poruchy, poruchy koagulace, porucha srážlivosti krve
Finnish Hyytymishäiriöt
Russian SVERTYVANIIA KROVI NARUSHENIIA, СВЕРТЫВАНИЯ КРОВИ НАРУШЕНИЯ
Korean 상세불명의 응고 결함
Croatian KRV, POREMEĆAJI KOAGULACIJE
Polish Zaburzenia krzepnięcia krwi
Hungarian véralvadási betegség k.m.n., Alvadás betegség, Alvadási zavarok, véralvadási betegség, Alvadási betegség, coagulopathia, véralvadási zavar (k.m.n.), Coagulopathiák, Alvadás, kóros, véralvadási betegség (k.m.n.)
Norwegian Koagulasjonsforstyrrelser, Koagulasjonsdefekter