Definition (NCI)
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A central nervous system disorder caused by demyelination within the central basis pontis of the brain. It is characterized by spastic quadriplegia, pseudobulbar palsy and encephalopathy. It is observed in patients with severe hyponatremia, particularly when the hyponatremia is corrected too rapidly.
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Definition (MSH)
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A demyelinating condition affecting the PONS and characterized clinically by an acute progressive QUADRIPLEGIA; DYSARTHRIA; DYSPHAGIA; and alterations of consciousness. Pathologic features include prominent demyelination in the central PONS with sparing of axons and neurons. This condition is usually associated with systemic disorders such as HYPONATREMIA; chronic ALCOHOLISM; LIVER FAILURE; severe BURNS; malignant NEOPLASMS; hemorrhagic PANCREATITIS; HEMODIALYSIS; and SEPSIS. The rapid medical correction of hyponatremia has been cited as a cause of this condition. (From Adams et al., Principles of Neurology, 6th ed, pp1125-6)
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Concepts |
Disease or Syndrome
(T047)
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MSH |
D017590
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ICD10 |
G37.2
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SnomedCT |
6807001
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English |
Central Pontine Myelinolysis, Myelinoclasis, Central Pontine, Pontine Myelinolysis, Central, Myelinolysis, Central Pontine, Central Pontine Myelinoclasis, central pontine myelinolysis (diagnosis), central pontine myelinolysis, Central pontine myelolysis, Myelinolysis, Central Pontine [Disease/Finding], central pontine myelinosis, Central pontine myelinolysis, Central pontine myelinolysis (disorder), myelinolysis; pontine, central, Central pontine myelinosis |
Swedish |
Myelinolys, central pontin
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Finnish |
Sentraalinen aivosillan myelinolyysi
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Russian |
VAROLIEVA MOSTA TSENTRAL'NYI MIELINOLIZ, DEMIELINIZATSIIA TSENTRAL'NAIA VAROLIEVA MOSTA, ОСМОТИЧЕСКИЙ ДЕМИЕЛИНИЗИРУЮЩИЙ СИНДРОМ, MIELINOLIZ TSENTRAL'NYI VAROLIEVA MOSTA, МИЕЛИНОЛИЗ ЦЕНТРАЛЬНЫЙ ПОНТИННЫЙ, MIELINOLIZ TSENTRAL'NYI PONTINNYI, МИЕЛИНОЛИЗ ЦЕНТРАЛЬНЫЙ ВАРОЛИЕВА МОСТА, OSMOTICHESKII DEMIELINIZIRUIUSHCHII SINDROM, ВАРОЛИЕВА МОСТА ЦЕНТРАЛЬНЫЙ МИЕЛИНОЛИЗ, ДЕМИЕЛИНИЗАЦИЯ ЦЕНТРАЛЬНАЯ ВАРОЛИЕВА МОСТА |
Japanese |
橋中心髄鞘崩壊, 髄鞘崩壊症-橋中心, 橋ミエリン溶解-中央, ミエリン溶解-橋中央, キョウチュウシンズイショウホウカイショウ, 橋中心髄鞘崩壊症, 橋中央ミエリン溶解 |
Korean |
중심성 교탈수초증
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Spanish |
Mielosis pontina central, Mielinólisis pontina central, mielinólisis pontina central (trastorno), mielinólisis pontina central, Mielinólisis Pontino Central |
Portuguese |
Mielinóse pontina central, Mielinólise pôntica central, Mielinólise Central da Ponte, Mielinólise Central Pontina |
French |
Myélolyse centrale du pont, Myélinolyse centropontique, Démyélinisation de la protubérance annulaire, Myélinolyse centrale du pont de Varole, Myélinolyse centrale du pont, Myélinolyse centropontine, Myélinolyse centro-pontine, Myélinolyse centro-pontique |
Italian |
Mielinolisi centrale pontina, Mielinolisi pontina centrale |
German |
Zentral pontine Myelinolyse, zentrale pontine Myelolyse, Myelinolyse, zentrale pontine, Pontine Myelinolyse, zentrale, Zentrale pontine Myelinolyse, Myelinoklasie, zentrale pontine |
Dutch |
centrale pontine myelinolyse, centrale pontine myelolyse, myelinolyse; pontien centraal, Centraal pontiene myelinolyse, Myelinolyse, centraal pontiene, Pontiene myelinolyse, centraal |
Czech |
Centrální pontinní myelinolýza, centrální pontinní myelinolýza, pons - myelinolýza |
Polish |
Mielinoliza mostu środkowa
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Hungarian |
Centralis pontin myelinolysis, Centralis pontin myelolysis |
Norwegian |
Sentral pontin myelinolyse
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