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Progressive Bulbar Paralysis
Aka: Progressive Bulbar Paralysis, Progressive Bulbar Palsy, Duchenne's Syndrome, Duchenne's Paralysis, Labioglossopharyngeal Paralysis, Labioglossolaryngeal Paralysis, Bulbar Paralysis
- Epidemiology
- Onset age 50-70 years
- Pathophysiology
- Subtype of Amyotrophic Lateral Sclerosis (ALS)
- Cranial Nerve motor nuclear atrophy, glial overgrowth
- Cranial Nerve 5
- Cranial Nerve 7
- Cranial Nerve 9
- Cranial Nerve 10
- Cranial Nerve 12
- Subcortical involvement of corticobulbar tracts
- Symptoms
- Drooling
- Difficult chewing
- Dysphagia
- Dysarthria
- Nasal regurgitation
- Signs
- Arm and leg spasticity
- Hyperactive reflexes
- Ophthalmoplegia
- Fasciculation of Tongue and lip Muscles
- Emotional lability
- Differential Diagnosis
- Acute Bulbar Paralysis
- Acute CNS vascular lesion (Hemorrhage or thrombosis)
- Acute Bulbar Polioencephalitis
- Chronic Bulbar Paralysis
- Syringobulbia
- Multiple Sclerosis
- Course
- Progresses to Aspiration Pneumonia, respiratory arrest
- Death in 1 to 3 years from onset