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Relapsing Polychondritis
Aka: Relapsing Polychondritis- Pathophysiology
- Not infectious
- Rare collagen vascular disease
- Affects at least 2 cartilaginous sites
- Findings: Symptoms and signs
- Auricle
- Pain and swelling
- Inflammation and local destruction
- Ear lobe is spared
- Sensorineural Hearing Loss may be associated
- Vertigo in 20% of cases
- Auricle
- Diagnosis
- Biopsy
- Management
- Systemic Corticosteroids
- Refer to Otolaryngology (ENT)
Polychondritis, Relapsing (C0032453) |
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Definition (MSH) | An acquired disease of unknown etiology, chronic course, and tendency to recur. It is characterized by inflammation and degeneration of cartilage and can result in deformities such as floppy ear and saddle nose. Loss of cartilage in the respiratory tract can lead to respiratory obstruction. |
Concepts | Disease or Syndrome (T047) |
MSH | D011081 |
ICD10 | M94.1 |
SnomedCT | 111256009, 85780006, 72275000 |
English | Polychondritides, Relapsing, Relapsing Polychondritides, Relapsing Polychondritis, Polychondritis, Chronic Atrophic, Atrophic Polychondritides, Chronic, Atrophic Polychondritis, Chronic, Chronic Atrophic Polychondritides, Chronic Atrophic Polychondritis, Polychondritides, Chronic Atrophic, RELAPSING POLYCHONDRITIS, relapsing polychondritis (diagnosis), relapsing polychondritis, Polychondritis, Relapsing, Polychondritis, Relapsing [Disease/Finding], polychondritis relapsing, chronic polychondritis, Systemic chondromalacia (disorder), Relapsing polychondritis, Chronic polychondritis, Systemic chondromalacia, Meyenburg's disease, Relapsing polychondritis (disorder), polychondritis; recrudescent [Brill-Zinsser], recrudescent [Brill-Zinsser]; polychondritis, Systemic chondromalacia -RETIRED-, Chondromalacia, systemic, Chronic atrophic polychondritis |
Spanish | policondritis recidivante, policondritis recidivante (trastorno), Policondritis atrófica crónica, Policondritis recidivante, policondritis crónica, policondritis crónica (trastorno), condromalacia sistémica - RETIRADO -, condromalacia sistémica - RETIRADO - (concepto no activo), condromalacia sistémica, Policondritis Atrófica Crónica, Policondritis Recurrente |
Dutch | recidiverende polychondritis, chronische atrofische polychondritis, polychondritis; recidiverend, recidiverend; polychondritis, Polychondritis, chronische atrofische, Polychondritis, recidiverende, Recidiverende polychondritis |
German | chronische atrophische Polychondritis, rezivierende Polychondritis, Panchondritis [Rezidivierende Polychondritis], Polychondritis chronica atrophicans, Polychondritis, rezidivierende |
Italian | Policondrite atrofica cronica, Policondrite cronica atrofica, Policondrite recidivante |
Portuguese | Policondrite recorrente, Policondrite atrófica crónica, Policondrite Atrófica Crônica, Policondrite Recidivante |
Swedish | Återfallspolykondrit |
Japanese | マンセイイシュクセイタハツセイナンコツエン, サイハツセイタハツセイナンコツエン, 軟骨炎-再発性多発性, 再発性多発性軟骨炎, 慢性萎縮性多発性軟骨炎, 多発性軟骨炎-再発性, 軟骨炎-慢性萎縮性多発性 |
Finnish | Uusiutuva monirustotulehdus |
Russian | POLIKHONDRIT RETSIDIVIRUIUSHCHII, ПОЛИХОНДРИТ РЕЦИДИВИРУЮЩИЙ |
Czech | Relabující polychondritida, Chronická atrofická polychondritida, relapsující polychondritida, recidivující polychondritida, relabující polychondritida, polychondritida recidivující |
Korean | 재발성 다발연골염 |
Polish | Zapalenie chrząstek nawracające, Zapalenie wielochrząstne nawracające, Zapalenie chrząstek zanikowe |
Hungarian | Krónikus atrophiás polychondritis, Recurrens polychondritis |
Norwegian | Polychondritis chronica atrophicans, Residiverende polykondritt |
French | Polychondrite chronique atrophiante, Polychondrite récidivante, Polychondrite à rechute |
Sources |
Derived from the NIH UMLS (Unified Medical Language System) |
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