II. Epidemiology

  1. Incidence: 1 in 2000 newborns

III. Associated Conditions

  1. Cleft Palate
  2. Ellis-van Crevald Syndrome
  3. Hallermann-Streiff Syndrome
  4. Pachyonychia Congenita Syndrome

IV. Management

  1. Erupted teeth require extraction especially if loose

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