II. Epidemiology

  1. Presents in infancy

III. Predisposing factors

  1. Other congenital anomalies
    1. Tracheoesophageal fistula
    2. Vascular Ring
  2. Prolonged intubation
  3. Prolonged Pediatric Gastroesophageal Reflux disease

IV. Signs

  1. Barking cough
  2. Expiratory Wheeze
  3. Provocative factors (increase Wheezing)
    1. Crying
    2. Feeding
    3. Cough
    4. Nebulized beta agonists

V. Diagnosis

  1. Bronchoscopy while child breathes spontaneously

VI. Management

  1. Supportive care
  2. Severe Tracheomalacia
    1. Tracheostomy
    2. CPAP

VII. Course

  1. Self limited
  2. Improves by age 12 to 24 months

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Ontology: Tracheomalacia (C0948187)

Definition (MSH) A congenital or acquired condition of underdeveloped or degeneration of CARTILAGE in the TRACHEA. This results in a floppy tracheal wall making patency difficult to maintain. It is characterized by wheezing and difficult breathing.
Definition (MSHCZE) Regresivní změna průdušnice s výrazným změknutím chrupavek. Může vzniknout např. lokálně z dlouhodobého útlaku např. strumou či při zánětech nebo v rámci celkové chondromalacie. Může způsobovat poruchy ventilace. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ )
Definition (NCI) A congenital or acquired abnormality of the wall of the trachea. In congenital cases, there is lack of rigidity in the cartilage of the tracheal wall. In acquired cases, the cartilage of the tracheal wall is degenerated, secondary to tracheostomy or prolonged presence of a breathing tube, or as a complication of a tracheoesophageal fistula surgical repair. Symptoms include stridor, noisy breathing, and upper respiratory infections.
Concepts Disease or Syndrome (T047)
MSH D055090
SnomedCT 266411000, 155627006, 95434006
Dutch tracheomalacie (excl. congenitaal), tracheomalacie
French Trachéomalacie (excl congénitale), Trachéomalacie, Chondromalacie de la trachée
German Tracheomalazie (ausschl kongenital), Chondromalazie der Luftröhre, Tracheomalazie
Italian Tracheomalacia (congenita esclusa), Condromalacia della trachea, Tracheomalacia, Condromalacia tracheale
Portuguese Traqueomalacia (excl. congénita), Traqueomalácia, Condromalacia da Traqueia
Spanish Traqueomalacia (excl congénita), Condromalacia de la Tráquea, Traqueomalacia, Condromalacia Traqueal, traqueomalacia (trastorno), traqueomalacia, Traqueomalasia
Japanese 気管軟化症(先天性を除く), キカンナンカショウ, キカンナンカショウセンテンセイヲノゾク, 気管軟化症
English Tracheomalacia, Tracheomalacias, Trachea Chondromalacia, Trachea Chondromalacias, Chondromalacia of Trachea, Tracheomalacia [Disease/Finding], tracheomalacia, Tracheomalacia (excl congenital), Tracheomalacia (disorder), Tracheomalacia (excluding congenital)
Czech Tracheomalacie, Tracheomalacie (kromě kongenitální), trachea - chondromalacie, tracheomalacie
Swedish Trakeomalaci
Polish Tracheomalacja, Rozmiękanie tchawicy wrodzone, Wiotkość tchawicy
Hungarian Tracheomalacia, Tracheomalacia (kivéve veleszületett)
Norwegian Brusksykdom i luftrør, Trakeomalasi, Kondromalasi i luftrør