Sarcoma
Sarcoma
search
Sarcoma
, Soft Tissue Sarcoma
See Also
Soft Tissue Mass
Definitions
Sarcoma
Cancer arrising in mesenchymal (connective) tissue
Derived from greek word "sar" meaning fleshy
Epidemiology
Age
More common in adults over age 35 years
Sarcomas represent 15% of childhood malignancy (esp. in extremities)
Types
Soft-tissue Sarcomas
Kaposi's Sarcoma
Hepatic angiosarcoma
Dermatofribosarcoma Protuberans
Synoviosarcoma
Rhabdomyosarcoma
Most common Soft Tissue Sarcoma in children
Leiomyosarcoma
Involves
Uterus
in adults
Involves
Retroperitoneum
in children
Liposarcoma
Rare adipose tumor (usually invades locally only)
Involves deep thigh or
Retroperitoneum
Fibrosarcoma
Most common Soft Tissue Sarcoma in age <1 year
Involves deep thigh or
Retroperitoneum
Vascular Sarcoma
Angiosarcoma
Hemangioendothelioma
Hemangiopericytoma
Bone Tumor
s
Ewing's Sarcoma
Osteogenic Sarcoma
Precautions
See
Soft Tissue Mass
for red flag findings
Delayed presentation is common (often >1 month from finding a
Soft Tissue Mass
)
Most Soft Tissue Sarcomas gradually enlarge without pain or constitutional symptoms
Evaluation
See
Soft Tissue Mass
(includes red flag findings and imaging)
Prognosis
Five year survival: 60% (depending on type, grading)
References
Achar (2022) Am Fam Physician 105(6): 602-12 [PubMed]
Type your search phrase here