Peds

Congenital Glaucoma

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Congenital Glaucoma

  • Epidemiology
  1. Rare pediatric eye disease
  2. Incidence: 1:12,500 live births
    1. Sporadic: 80-90%
    2. Familial: 10-20%
  3. Onset under age 1 year
  4. Bilateral eyes involved in 75% cases
  • Pathophysiology
  1. Intraocular Pressure abnormally increased
  2. Damages the Optic Nerve
  • Etiology
  1. Congenital Cataract surgery
  2. Congenital Infections
    1. TORCH Virus (especially Rubella)
  3. Sturge Weber Syndrome
  4. Retinopathy of Prematurity
  5. Neurofibromatosis
  6. Aniridia
  7. Aphakia
  8. Steroid induced
  9. Uveitis
  • Symptoms (presents during first months of life)
  1. Epiphora (chronic tearing) or other Lacrimation
  2. Eye discomfort
  3. Photophobia (light sensitivity)
  4. Excessive Eyelid squeezing (blepharospasm)
  • Signs
  1. Optic Nerve "cupping"
  2. Buphthalmos
    1. Injected Red Eye
    2. Hazy or "steamy" Cornea (Corneal Opacification)
    3. Swollen eye
  • Differential Diagnosis
  • Management
  1. Surgical Direct communication made between
    1. Anterior chamber
    2. Aqueous Humor draining system (Schlemm's canal)
  2. Long term Ophthalmology follow-up