Peds

Klippel-Trenaunay-Weber Syndrome

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Klippel-Trenaunay-Weber Syndrome, Parkes-Weber Syndrome

  • Signs
  1. Port-Wine Stain over an extremity
  2. Extremity soft tissue and bony hypertrophy
  • Evaluation
  1. Measure length and girth of extremity every 3-6 month
  2. If extremity elongation noted:
    1. Evaluate for arteriovenous fistula
    2. Evaluate for venous atresia