Pulmonology Book


Pulmonary Langerhans Cell Granulomatosis

Aka: Pulmonary Langerhans Cell Granulomatosis, Eosinophilic Granuloma, Pulmonary Histiocytosis X, Unifocal Langerhans Cell Histiocytosis
  1. See Also
    1. Langerhans Cell Histiocytosis
  2. Pathophysiology
    1. Dendritic Cell disorder
  3. Associated Conditions
    1. Letterer-Siwe
    2. Hand-Schuller-Christian Syndrome
    3. Histiocytosis X with Bone involvement
  4. Epidemiology
    1. Ages 20-40 years old
    2. Prior Tobacco use (90%)
  5. Signs
    1. See Interstitial Lung Disease
  6. Complications
    1. Pneumothorax (10-30%)
    2. Diabetes Insipidus
    3. Lytic bone lesions (5-10%)
  7. Management
    1. None available
  8. Coarse
    1. Unpredictable prognosis
    2. Mortality 2-6%

Eosinophilic Granuloma (C0014461)

Definition (MSH) The most benign and common form of Langerhans-cell histiocytosis which involves localized nodular lesions predominantly of the bones but also of the gastric mucosa, small intestine, lungs, or skin, with infiltration by EOSINOPHILS.
Definition (MSHCZE) Lokalizovaná forma granulomatózy z Langerhansových buněk (histiocytózy X). Postiženy mohou být plíce či kosti (osteolytický nádor), průběh je relativně benigní. Histologicky jsou četné eozinofily. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ )
Definition (NCI) A clinical variant of Langerhans cell histiocytosis characterised by unifocal involvement of a bone (most often), skin, or lung. Patients are usually older children or adults usually presenting with a lytic bone lesion. The etiology is unknown. Morphologically, eosinophilic granuloma is characterised by the presence of Langerhans cells in a characteristic milieu which includes histiocytes, eosinophiles neutrophiles, and small, mature lymphocytes.
Definition (CSP) most benign clinical form of Langerhans-cell histiocytosis, which involves localized nodular lesions of the gastric mucosa, small intestine, bones, lungs, or skin, with infiltration by eosinophils; the proliferating cell that appears to be responsible for the clinical manifestations is the Langerhans cell.
Concepts Pathologic Function (T046)
MSH D004803
ICD10 K13.4, C96.6
SnomedCT 77239009, 128810002, 129000002
English Eosinophilic Granuloma, Eosinophilic Granulomas, Granuloma, Eosinophilic, Granulomas, Eosinophilic, EOSINOPHILIC GRANULOMA, Eosinophilic xanthom granuloma, Unifocal Langerhans Cell Histiocytosis, eosinophilic granuloma (diagnosis), eosinophilic granuloma, unifocal eosinophilic granuloma (diagnosis), unifocal eosinophilic granuloma, Eosinophilic Granuloma [Disease/Finding], granuloma eosinophilic, Eosinophilic granuloma (morphologic abnormality), Eosinophilic granuloma, Eosinophilic xanthomatous granuloma, Eosinophilic granuloma (clinical), eosinophilic; granuloma, granuloma; eosinophilic, Eosinophilic granuloma -RETIRED-, Eosinophilic Xanthomatous Granuloma
Portuguese GRANULOMA EOSINOFILO, Granuloma eosinófilo, Granuloma Eosinófilo
Spanish GRANULOMA EOSINOFILO, Granuloma eosinofílico, granuloma eosinofílico xantomatoso, granuloma eosinofílico (concepto no activo), granuloma eosinofílico, granuloma eosinófilo, Granuloma Eosinófilo
German EOSINOPHILES GRANULOM, eosinophiles Granulom, Eosinophiles Granulom, Granulom, eosinophiles
Swedish Eosinofilt granulom
Czech eozinofilní granulom, Eozinofilní granulom
Finnish Eosinofiilinen granulooma
French GRANULOME EOSINOPHILIQUE, Granulome éosinophile
Dutch eosinofiel granuloom, eosinofiel; granuloom, granuloom; eosinofiel, Eosinofiel granuloom, Granuloma eosinophilicum
Japanese コウサンキュウセイニクゲシュ, 肉芽腫-好酸球性, エオシン好性肉芽腫, 好酸球性肉芽腫, 好酸球肉芽腫
Polish Ziarniniak kwasochłonny
Hungarian Eosinophil granuloma
Norwegian Granulom, eosinofilt, Eosinofilt granulom
Italian Granuloma eosinofilo
Derived from the NIH UMLS (Unified Medical Language System)

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