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Pectus Excavatum
Aka: Pectus Excavatum, Funnel Breast, Trichterbrust- Epidemiology
- Incidence: 0.5 to 2%
- Gender predominance: Boys (3:1 ratio)
- Causes
- Rickets
- Scurvy
- Marfan's Syndrome
- Occupationally acquired
- Example: Cobbler's Chest (shoe pressed against chest)
- Associated Conditions
- Scoliosis
- Congenital Heart Disease
- Severe childhood Asthma
- Pathophysiology
- Deformed lower costal cartilages
- Results in retraction of chest wall toward spine
- Inferior Sternum
- Xiphoid process
- Signs
- Opposite of Pectus Carinatum
- Mild: Oval pit near infrasternal notch
- Severe: Sinking of entire lower Sternum
- Complications
- Restrictive Lung Disease in severe cases
- References
- Degowin (1987) Bedside Exam, Macmillan, p. 274
- Murray and Nadel (2000) Respiratory Medicine, p. 2364-6
Congenital pectus excavatum (C0016842) |
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Definition (MSHCZE) | vrozená vada, při níž je přední stěna hrudníku vtažena dovnitř (trychtýřovitě, též pectus infundibuliforme) s možným ovlivněním činnosti srdce a plic. Léčí se dechovými cvičeními, ev. chirurgicky. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ ) |
Definition (MSH) | A developmental anomaly in which the lower sternum is posteriorly dislocated and concavely deformed, resulting in a funnel-shaped thorax. |
Concepts | Congenital Abnormality (T019) , Disease or Syndrome (T047) |
MSH | D005660 |
ICD9 | 754.81 |
ICD10 | Q67.6 |
SnomedCT | 391982004, 123260001, 391986001, 74708002, 45469009, 268348002, 157002004 |
English | Chest, Funnel, Chests, Funnel, Excavatum, Pectus, Funnel Chest, Funnel Chests, Pectus Excavatum, Pectus excavatum, FUNNEL CHEST, PECTUS EXCAVATUM, pectus excavatum (diagnosis), pectus excavatum, Funnel breast, Hollowed breast, Funnel Chest [Disease/Finding], pectus recurvatum, funnel breast, excavatum pectus, chested funnel, congenital pectus excavatum, disorders excavatum pectus, Pectus recurvatum, Trichterbrust, Pectus excavatum (disorder), Cobbler's chest (disorder), Congenital pectus excavatum, Congenital funnel chest, Congenital pectus excavatum (disorder), funnel chest, congenital; funnel chest, excavatum; pectus, funnel chest; congenital, pectus; excavatum, Cobbler's chest -RETIRED-, Pectus excavatum [ambiguous][dup] (disorder), Funnel chest, Cobbler's chest |
Dutch | trechterborst, cobbler's chest (schoenmakersborst), ingezakte borst, schoenmakersborst (pectus excavatum), congenitaal; trechterborst, excavatum; pectus, pectus; excavatum, trechterborst; congenitaal, pectus excavatum, Pectus excavatum, Schoenmakersborst |
French | Poitrine creuse, Cuvette sternale, Thorax en entonnoir, Pectus excavatum |
German | Schusterbrust, eingefallene Brust, Pectus excavatum, Trichterbrust |
Italian | Torace da calzolaio, Petto incavato, Torace ad imbuto, Petto scavato, Pectus excavatum, Torace a imbuto |
Portuguese | Peito em funil, Tórax em funil, Tórax de sapateiro, Peito de Sapateiro, Tórax Escavado, Peito escavado, Pectus Excavatum, Tórax em Funil |
Spanish | Tórax excavado, Tórax de Cobbler, Pecho en embudo, Tórax en embudo, pectus excavatum congénito, pecho en embudo congénito, pecho excavado, pectus recurvatum, pectus excavatum (trastorno), tórax de Cobbler - RETIRADO -, tórax de Cobbler - RETIRADO - (concepto no activo), tórax infundibuliforme, pectus excavatum, Tórax de Zapatero, Tórax en Embudo Congénito, Tórax Excavado, tórax en embudo congénito (trastorno), tórax en embudo congénito, Pectus excavatum, Pectus Excavatum, Tórax en Embudo |
Japanese | コブラー胸, 先天性漏斗胸, ロウトムネ, コブラーキョウ, センテンセイロウトキョウ, カンボツキョウ, ロウトキョウ, カンボツムネ, 陥凹胸, 漏斗胸, 靴匠胸, 靴工胸 |
Swedish | Trattbröst |
Czech | hrudník vpáčený, pectus excavatum, Nálevkovitý hrudník, Vpadlý hrudník, Pectus excavatum, pectus infundibuliforme, hrudník nálevkovitý |
Finnish | Kuopparinta |
Russian | VORONKOOBRAZNAIA GRUD', GRUD' SAPOZHNIKA, GRUDNAIA KLETKA VORONKOOBRAZNAIA, ВОРОНКООБРАЗНАЯ ГРУДЬ, ГРУДНАЯ КЛЕТКА ВОРОНКООБРАЗНАЯ, ГРУДЬ САПОЖНИКА |
Korean | 오목가슴 |
Polish | Klatka piersiowa lejkowata |
Hungarian | Emlő tölcsér, Cobbler-mellkas, Emlő hollowed, Pectus excavatum, Susztermellkas |
Norwegian | Traktbryst, Pectus excavatum |
Sources |
Derived from the NIH UMLS (Unified Medical Language System) |
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