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Chemodectoma
Aka: Chemodectoma, Glomus tumor- Epidemiology
- Most common in 40 to 50 year old women
- Pathophysiology
- Neuroendocrine tumor arising from from glomus bodies
- Jugular bulb origin or
- Middle ear neural plexus
- Tympanic Membrane invasion follows Hearing Loss
- May involve Cranial Nerves
- Neuroendocrine tumor arising from from glomus bodies
- Symptoms
- Pulsating Tinnitus
- Hearing Loss
- Signs
- Dark blue, purple or red-blue mass behind TM
- Diagnosis
- Differential Diagnosis
- Anomalous Carotid Artery
- Anomalous jugular bulb
- Management
- Do not biopsy (very vascular)
- Surgical excision
Glomus Tumor (C0017653) |
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Definition (NCI) | A rare benign or malignant mesenchymal neoplasm arising from cells that resemble the modified smooth muscle cells of the glomus body. The majority of glomus tumors occur in the distal extremities. |
Definition (MSH) | A blue-red, extremely painful vascular neoplasm involving a glomeriform arteriovenous anastomosis (glomus body), which may be found anywhere in the skin, most often in the distal portion of the fingers and toes, especially beneath the nail. It is composed of specialized pericytes (sometimes termed glomus cells), usually in single encapsulated nodular masses which may be several millimeters in diameter (From Stedman, 27th ed). CHEMODECTOMA, a tumor of NEURAL CREST origin, is also sometimes called a glomus tumor. |
Concepts | Neoplastic Process (T191) |
MSH | D005918 |
ICD10 | M8711/0 |
SnomedCT | 189193002, 393567008, 10438002, 403969002 |
English | Glomus Tumors, Tumor, Glomus, Tumors, Glomus, Glomus Tumor, Glomus Tumor [Disease/Finding], tumor glomus, glomus tumor, glomus tumour, glomus tumors, Glomus tumour (disorder), Glomus tumor, Glomus tumour, Glomus tumor (disorder), Glomus tumor (morphologic abnormality), Glomus Neoplasm |
Dutch | glomus tumor, glomustumor, Gezwel, glomus-, Glomusgezwel |
French | Tumeur du glomus, Tumeur glomique, Angiomyoneurome |
German | Glomus Tumor, Glomustumor |
Spanish | Tumor glómico, tumor glómico (anomalía morfológica), tumor glómico (trastorno), tumor glómico, Glomangioma, Tumor Glómico |
Japanese | グロームス腫瘍, グロームスシュヨウ |
Swedish | Nysttumör |
Czech | glomangiom, Glomus tumor |
Finnish | Glomuskasvain |
Russian | GLOMUSA OPUKHOL', GLOMANGIOMA, GLOMUSA NOVOOBRAZOVANIE, ГЛОМАНГИОМА, ГЛОМУСА НОВООБРАЗОВАНИЕ, ГЛОМУСА ОПУХОЛЬ |
Croatian | GLOMUS TUMOR |
Polish | Guz kłębka skórnego, Kłębczak |
Hungarian | Glomus tumor |
Italian | Tumore del glomo, Tumore glomico |
Norwegian | Glomussvulst, Glomustumor |
Portuguese | Tumor glómico, Tumor Glômico |
Sources |
Derived from the NIH UMLS (Unified Medical Language System) |
Extra-Adrenal Paraganglioma (C0030422) |
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Definition (MSH) | A relatively rare, usually benign neoplasm originating in the chemoreceptor tissue of the CAROTID BODY; GLOMUS JUGULARE; GLOMUS TYMPANICUM; AORTIC BODIES; and the female genital tract. It consists histologically of rounded or ovoid hyperchromatic cells that tend to be grouped in an alveolus-like pattern within a scant to moderate amount of fibrous stroma and a few large thin-walled vascular channels. (From Stedman, 27th ed) |
Definition (NCI) | A benign or malignant paraganglioma arising from sympathetic or parasympathetic paraganglia outside the adrenal gland. |
Concepts | Neoplastic Process (T191) |
MSH | D010236 |
ICD10 | M8693/1 |
SnomedCT | 189744003, 134298001, 302834008, 51747000 |
English | Chemodectoma, Nonchromaffin Paragangliomas, Paraganglioma, Nonchromaffin, Paragangliomas, Nonchromaffin, Paraganglioma, Non-Chromaffin, Paraganglioma, Extra-Adrenal, Extra-Adrenal Paragangliomas, Non-Chromaffin Paraganglioma, Non-Chromaffin Paragangliomas, Paraganglioma, Extra Adrenal, Paraganglioma, Non Chromaffin, Paragangliomas, Extra-Adrenal, Paragangliomas, Non-Chromaffin, Nonchromaffin Paraganglioma, Extra-adrenal paraganglioma, NOS, Extra-Adrenal Paraganglionic Neoplasm, Extra-Adrenal Paraganglioma, PARAGANGLIOMAS, FAMILIAL NONCHROMAFFIN, 1, CHEMODECTOMAS, [M]Extra-adrenal paragangl.NOS, [M]Extra-adrenal paraganglioma, NOS, Extra-adrenal paragangl.NOS, Paraganglioma, Extra-Adrenal [Disease/Finding], Extra-adrenal paraganglioma NOS, chemodectoma, Paragangliomas, Familial Nonchromaffin, 1, Chemodectomas, [M]Chemodectoma, [M] (Extra-adrenal paraganglioma, NOS) or (chemodectoma), [M] (Extra-adrenal paraganglioma, NOS) or (chemodectoma) (disorder), [M]Extra-adrenal paraganglioma, NOS (morphologic abnormality), extra-adrenal paraganglioma, extra-adrenal paraganglioma (diagnosis), neoplasm of paraganglioma extra-adrenal, Extra-adrenal paraganglioma, Nonchromaffin paraganglioma, Non-chromaffin paraganglioma, Extra-adrenal paraganglioma (disorder), Extra-adrenal paraganglioma (morphologic abnormality), Nonchromaffin paraganglioma, NOS, Extraadrenal Paraganglioma |
Japanese | 非クロム親和性傍神経細胞腫, ヒクロムシンワセイボウシンケイサイボウシュ, 化学感受体腫, 傍神経節腫-非クロム親和性, ケモデクトーマ, 副腎外パラガングリオーマ, 非クロム親和性パラガングリオーマ, 非クロム親和性傍神経節腫, パラガングリオーマ-副腎外, パラガングリオーマ-非クロム親和性, 傍神経節腫-副腎外, 副腎外傍神経節腫 |
Swedish | Paragangliom, extraadrenalt |
Czech | paragangliom nechromafinní, chemodektom, Chemodektom |
Finnish | Ekstra-adrenaalinen paragangliooma |
Russian | PARAGANGLIOMA NEKHROMAFFINNAIA, PARAGANGLIOMA VNENADPOCHECHNIKOVAIA, KHEMODEKTOMA, ПАРАГАНГЛИОМА ВНЕНАДПОЧЕЧНИКОВАЯ, ПАРАГАНГЛИОМА НЕХРОМАФФИННАЯ, ХЕМОДЕКТОМА |
Italian | Paraganglioma non cromaffine, Chemodectoma, Paraganglioma extra adrenale |
Croatian | Not Translated[Paraganglioma, Extra-Adrenal] |
Spanish | paraganglioma extrasuprarrenal (trastorno), paraganglioma extrasuprarenal (trastorno), paraganglioma extrasuprarenal, paraganglioma extradrenal, paraganglioma extrasuprarrenal (anomalía morfológica), paraganglioma extrasuprarrenal, paraganglioma no cromafín, quemodectoma, Quimiodectoma, Paraganglioma Extraadrenal, Paraganglioma no Cromafínico, Quemodectoma |
Polish | Przyzwojak nienadnerczowy, Przyzwojak pozanadnerczowy, Przyzwojak niechromochłonny |
Hungarian | Chemodectoma |
Norwegian | Ekstraadrenalt paragangliom |
Portuguese | Paraganglioma não Cromafim, Paraganglioma Extrassuprarrenal, Paraganglioma não Cromafínico, Quimiodectoma |
Dutch | chemodectoom, Chemodectoma, Paraganglioma, extra-adrenaal, Paraganglioma, non-chroomaffien, extra-adrenaal paraganglioma |
French | Paragangliome non chromaffine, Paragangliome extra-surrénalien, Chémodectome, Paragangliome extrasurrénalien |
German | Chemodektom, Paragangliom, extraadrenales, Paragangliom, nichtchromaffines |
Sources |
Derived from the NIH UMLS (Unified Medical Language System) |
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