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Left Ventricular Noncompaction
Aka: Left Ventricular Noncompaction, Noncompaction Cardiomyopathy, Left Ventricular Noncompaction Cardiomyopathy
- Epidemiology
- Uncommon congenital Cardiomyopathy (<1% of population)
- Pathophysiology
- Disordered in-utero development of mature heart Muscle
- Increased trabeculation of Myocardium
- Development of increased intertrabecular recesses within the left ventricle
- Results in Left Ventricular Dysfunction
- Heart Failure
- Arrhythmia
- Thromboembolic disease
- Sudden Cardiac Death
- Findings
- See Congestive Heart Failure
- Diagnosis
- Echocardiogram
- Initial, first-line test
- Cardiac MRI
- Confirms diagnosis
- Management
- See Congestive Heart Failure
- Anticoagulation indications
- Atrial Fibrillation
- Decreased systolic function
- Systemic Thromboembolism or intracardiac thrombus
- References
- Brieler (2017) Am Fam Physician 96(10):640-6 [PubMed]
- Stacey (2015) Curr Heart Fail Rep 12(1):61-7 [PubMed]