Surgery Book

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Congenital Lymphedema

Aka: Congenital Lymphedema, Lymphedema Congenita, Milroy's Disease
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  1. Epidemiology
    1. Onset within first two years of life
  2. See Also
    1. Lymphedema
  3. Definition
    1. Severe Lymphedema onset at birth or as infant
    2. Milroy's Disease is a famial subtype
  4. Signs
    1. Lower extremity edema
      1. Right leg more often affected
      2. Bilateral involvement in 25% of cases
    2. Involves foot dorsum up to knee
  5. Associated Conditions
    1. Swelling of external genitalia
    2. Intestinal lymphangiectasia, protein-losing Enteropathy
    3. Cystic Hygroma
    4. Pulmonary lymphangiectasia
  6. References
    1. Sabiston (1997) Surgery, Saunders, p.1574-5
    2. Rockson (2001) Am J Med 110:288-95

Milroy Disease (C1704423)

Concepts Disease or Syndrome (T047)
MSH D008209
SnomedCT 195489008, 399889006, 75127007, 157017000, 268355000, 205544008, 234098006
English Congenital lymphedema, Milroy's Disease, Milroys Disease, Milroy's disease, NONNE-MILROY-MEIGE SYNDROME, Congenital lymphoedema, Infantile lymphedema (praecox), Infantile lymphedema(praecox), Infantile lymphoedema (praecox), Infantile lymphoedema(praecox), Milroy Disease, PRIMARY CONGENITAL LYMPHEDEMA, PCL, NONNE-MILROY LYMPHEDEMA, MILROY DISEASE, LYMPHEDEMA, EARLY-ONSET, MILROYS DIS, MILROY DIS, Primary (congenit.)lymphedema, Primary (congenit.)lymphoedema, Primary (congenital) lymphedema, Primary (congenital) lymphoedema, Congenital lymphoedema (disorder), Milroy's disease (diagnosis), Lymphedema congenital, Lymphoedema congenital, LYMPHEDEMA, HEREDITARY, IA, Nonne Milroy Disease, Nonne Milroy Meige Disease, Nonne-Milroy-Meige Disease, Nonne-Milroy Disease, LMPH1A, Hereditary lymphedema type I (disorder), Hereditary lymphedema type I, Hereditary lymphoedema type I, Milroy lymphedema, Milroy lymphoedema, Nonne-Milroy lymphedema, Nonne-Milroy lymphoedema, Primary congenital lymphedema, Primary congenital lymphoedema, Milroy; edema, Milroy, Nonne-Milroy, edema; Milroy, Milroy's disease (disorder)
Italian Linfedema congenito, Malattia di Milroy
Dutch congenitaal lymfoedeem, lymfoedeem congenitaal, ziekte van Milroy, Milroy; oedeem, oedeem; Milroy, lymfoedeem, congenitaal, Milroy-ziekte
German Lymphoedem kongenital, Milroykrankheit, Milroy-Krankheit, kongenitales Lymphoedem
Japanese ミルロイ病, ﾐﾙﾛｲﾋﾞｮｳ, 先天性リンパ浮腫, ｾﾝﾃﾝｾｲﾘﾝﾊﾟﾌｼｭ
Spanish Congenital lymphedema, Milroy's disease, Congenital lymphoedema, enfermedad de Milroy (trastorno), enfermedad de Milroy, linfedema congénito, linfedema hereditario tipo I (trastorno), linfedema hereditario tipo I, Linfedema congénito, Enfermedad de Milroy
French Maladie de Milroy, Lymphoedème congénital, Syndrome de Meige-Milroy-Nonne, Trophoedème, Éléphantiasis familial de Milroy
Czech Lymfedém vrozený, Vrozený lymfedém, Milroyova nemoc
Hungarian Milroy-betegség, Veleszületett nyirokoedema, Kongenitális lymphoedema, Veleszületett lymphoedema
Portuguese Linfedema congénito, Doença de Milroy
Sources
Derived from the NIH UMLS (Unified Medical Language System)


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