Hematology and Oncology Book

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Purpura fulminans

Aka: Purpura fulminans
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  1. Pathophysiology
    1. Associated with Disseminated Intravascular Coagulopathy
    2. Possible etiologies
      1. Severe bacterial infection (Meningococcemia)
      2. Protein C Deficiency
      3. Protein S Deficiency
  2. Signs
    1. See also Disseminated Intravascular Coagulopathy
    2. Minimal inflammation
    3. Rapidly progressive Purpura
      1. Microvascular thrombosis in Dermis
      2. Perivascular Hemorrhage
      3. Necrotic gangrene
  3. Prognosis
    1. Frequently lethal condition

Purpura Fulminans (C0085650)

Definition (MSH) A severe, rapidly fatal reaction occurring most commonly in children following an infectious illness. It is characterized by large, rapidly spreading skin hemorrhages, fever, or shock. Purpura fulminans often accompanies or is triggered by DISSEMINATED INTRAVASCULAR COAGULATION.
Concepts Disease or Syndrome (T047)
MSH D055665, D011695
ICD10 D65
SnomedCT 13507004
English PURPURA FULMINANS, purpura fulminans, purpura fulminans (diagnosis), Fulminans, Purpura, Purpura Fulminans, Purpura Fulminans [Disease/Finding], fulminans purpura, Purpura fulminans, Purpura fulminans (disorder), fulminans; purpura, purpura; fulminans, Purpura, fulminans
Japanese 電撃性紫斑病, デンゲキセイシハンビョウ
Czech Purpura fulminans, purpura fulminans, fulminantní purpura
Spanish Purpura Fulminante, Púrpura Fulminante, púrpura fulminante (trastorno), púrpura fulminante, Purpura fulminante
French Purpura fulminans
Italian Porpora fulminante, Purpura Fulminans
Russian ПУРПУРА МОЛНИЕНОСНАЯ, PURPURA MOLNIENOSNAIA
German Purpura fulminans
Swedish Purpura fulminans
Portuguese Púrpura Fulminante, Purpura Fulminans, Púrpura fulminante
Polish Plamica piorunująca
Hungarian Purpura fulminans
Dutch fulminans; purpura, purpura; fulminans, purpura fulminans, Purpura fulminans
Sources
Derived from the NIH UMLS (Unified Medical Language System)


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