II. Epidemiology

  1. Uncommon cause of Chronic Pancreatitis
  2. Average age: 63 years (More than 80% are over age 50 years)
  3. Male gender predominance by 2 fold

III. Symptoms: Presentations

  1. Jaundice (>60%)
  2. Abdominal Pain (>30%)

V. Diagnosis

  1. IgG4 titer
    1. Significantly increased in Autoimmune Pancreatitis
  2. CT Abdomen
    1. Diffuse pancreatitic involvement

VI. Management

  1. Prednisone 40 mg/day for 1 week and then taper dose down by 5 mg weekly

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